先天性后鼻孔闭锁并额外鼻孔鼻腔畸形1例  

One case of congenital choanal atresia with additional nostril nasal cavity malformation

作　　者：李春苗[1] 李颖[1] 韩富根 段清川 僧东杰 LI Chunmiao;LI Ying;HAN Fugen;DUAN Qingchuan;SENG Dongjie(Department of Otorhinolaryngology Head and Neck Surgery,Children's Hospital Affiliated to Zhengzhou University,Henan Children's Hospital,Zhengzhou Children's Hospital,Zhengzhou,450018,China;Department of Otorhinolaryngology Head and Neck Surgery, Beijing Children's Hospital, Capital Medical University National Center for Children's Health)

机构地区：[1]郑州大学附属儿童医院河南省儿童医院,郑州儿童医院耳鼻咽喉头颈外科,郑州450018 [2]国家儿童医学中心,首都医科大学附属北京儿童医院耳鼻咽喉头颈外科

出　　处：《临床耳鼻咽喉头颈外科杂志》2024年第11期1077-1080,共4页Journal of Clinical Otorhinolaryngology Head And Neck Surgery

基　　金：国家区域医疗中心开放课题资助(No:NRMC0105)。

摘　　要：本文报道河南省儿童医院收治的1例先天性后鼻孔闭锁并额外鼻孔鼻腔畸形患儿。女,43 d,因“生后喘憋伴张口呼吸、吃奶受限”为代主诉入院,入院后完善纤维鼻咽镜、CT、基因检测并结合体检结果,诊断为:双侧先天性后鼻孔膜性闭锁、先天性额外鼻孔鼻腔畸形、鼻腔狭窄,于全身麻醉下行鼻内镜下双侧后鼻孔成形术及左侧前鼻孔成形术。术后患儿术后恢复良好。This article reports a case of congenital choanal atresia with additional nostril and nasal deformities admitted to Henan Children's Hospital.A 43-day-old female patient was admitted to the hospital because of wheezing with mouth opening breathing and restricted feeding after birth'.The patient was diagnosis as bilateral congenital posterior nostril membranous atresia,congenital extra nostril nasal deformity and nasal stenosis by fiberoptic nasopharyngoscopy,CT,gene detection,and physical examination results.Under general anesthesia,endoscopic bilateral posterior nostril plasty and left anterior nostril plasty were performed.The child recovered well after operation.

关 键 词：后鼻孔闭锁 鼻畸形 通气管 先天性 

分 类 号：R322.3[医药卫生—人体解剖和组织胚胎学]