《血友病患者出血急诊管理中国指南》解读  

Interpretation of Chinese guidelines on the management of bleeding events of hemophilia patients in emergency

作　　者：迟骋[1] 郭杨[1] 杨仁池 CHI Cheng;GUO Yang;YANG Renchi(Department of Emergency,Peking University People's Hospital,Beijing,100044,China;Institute of Hematology and Blood Diseases Hospital,Chinese Academy of Medical Sciences)

机构地区：[1]北京大学人民医院急诊科,北京100044 [2]中国医学科学院血液病医院(中国医学科学院血液学研究所)

出　　处：《临床血液学杂志》2024年第11期759-761,共3页Journal of Clinical Hematology

基　　金：中国医学科学院医学与健康科技创新工程项目(No:2021-I2M-1-003)。

摘　　要：血友病是一种罕见的X染色体连锁隐性遗传性出血性疾病,出血是血友病患者最常见的急症,也是血友病患者致死、致残、影响生活质量的主要因素。快速识别和规范诊疗对于改善患者预后具有重要意义。急诊科是血友病患者出血的主要首诊科室,血友病出血急诊处置流程复杂,常常需要多学科联合诊疗和综合管理。近期,由中华医学会血液学分会血栓与止血学组和中国血友病协作组共同制定了《血友病患者出血急诊管理中国指南》。为更好地指导临床实践,本文拟对该指南进行解读。Hemophilia is a rare X-linked recessive hemorrhagic disease.Bleeding is the most common complication of hemophilia and is also the main factor leading to death,disability,or reduced quality of life for hemophilia patients.Rapid identification and standardized treatment of bleeding are of great significance in improving the prognosis of patients.The emergency department is the primary department for hemophilia patients with bleeding.The emergency treatment process for hemophilia hemorrhage is complex and often requires multidisciplinary management.Recently,the Thrombus and Hemostasis Group of the Hematology Branch of the Chinese Medical Association and the China Hemophilia Collaboration Group jointly formulated the Chinese guidelines on the management of bleeding events of hemophilia patients in emergency.In order to guide clinical practice,this paper intends to interpret the guidelines.

关 键 词：血友病 出血 急诊 管理 

分 类 号：R554.1[医药卫生—血液循环系统疾病]