转甲状腺素蛋白心脏淀粉样变合并肺受累一例  

A case of transthyretin cardiac amyloidosis with pulmonary involvement

作　　者：卜星彭 王晓艳[1] 杨文静 马晓萌 沙硕 陈还珍[3] Bu Xingpeng;Wang Xiaoyan;Yang Wenjing;Ma Xiaomeng;Sha Shuo;Chen Huanzhen(First Clinical Medical College,Shanxi Medical University,Taiyuan030001,China;Department of General Medicine,Shanxi Bethune Hospital,Shanxi Academy of Medical Sciences,Tongji Shanxi Hospital,Taiyuan030032,China;Department of Cardiology,First Hospital of Shanxi Medical University,Taiyuan030001,China)

机构地区：[1]山西医科大学第一临床医学院,太原030001 [2]山西白求恩医院(山西医学科学院同济山西医院)综合医疗科,太原030032 [3]山西医科大学第一医院心血管内科,太原030001

出　　处：《中华心力衰竭和心肌病杂志（中英文）》2024年第3期207-210,共4页Chinese Journal of Heart Failure and Cardiomyopathy

摘　　要：在肺部受累的系统性淀粉样变患者中,最常见的是免疫球蛋白轻链淀粉样变(AL)型,而转甲状腺素蛋白淀粉样变(ATTR)型很少报道。本文报道一例女性患者确诊转甲状腺素蛋白型心脏淀粉样变(ATTR-CA)合并肺受累,口服氯苯唑酸治疗,1年后复诊肺部淀粉样变发生进展。In patients with systemic amyloidosis involving the lungs,the most common type is immunoglobulin light chain amyloidosis(AL),while the transthyretin(ATTR)type is rarely reported.This article reported a female patient who was diagnosed with transthyretin cardiac amyloidosis(ATTR-CA)with lung involvement and received oral treatment with tafamidis.After one year of follow-up,pulmonary amyloidosis progressed.

关 键 词：转甲状腺素蛋白 淀粉样变 心肌病 间质性肺病 

分 类 号：R597.2[医药卫生—内科学]