主动脉弓离断合并主—肺动脉间隔缺损的心血管造影诊断  

Angiocardiographic Diagnosis of Interrupted Aortic Arch With Aortopulmonary Septal Defect

作　　者：张庆桥[1] 蒋世良[1] 凌坚[1] 徐仲英[1] 张岩[1] 谢若兰[1] 

机构地区：[1]中国医学科学院中国协和医科大学心血管病研究所阜外心血管病医院放射科,北京市100037

出　　处：《中国循环杂志》2002年第5期377-379,共3页Chinese Circulation Journal

摘　　要：目的 :评价主动脉弓离断 (IAA)合并主—肺动脉间隔缺损 (APSD)的心血管造影表现 ,提高诊断准确性。　　方法 :回顾性分析 4例患者的心导管检查和心血管造影资料。　　结果 :心导管检查 4例均提示重度肺动脉高压、主动脉弓畸形、动脉导管未闭 (PDA)及主—肺动脉根部有交通。心血管造影 4例均诊断为IAA合并APSD ,其中 1例合并右肺动脉起自升主动脉。手术治疗 1例 ,为IAA (Ⅰ型 )合并APSD (Ⅱ型 )及右肺动脉起自升主动脉。　　结论 :心血管造影是诊断IAA合并APSD的可靠方法。Objective:To evaluate the imaging findings of interrupted aortic arch(IAA)complicated by aortopulmonary septal defect(APSD)in order to improve the diagnostic accuracy. Methods:Data from four patients on cardiac catheterization and angiocardiography were analyzed retrospectively. Results:Cardiac catheterization suggested severe pulmonary hypertension,anomaly of aortic arch,patent ductus arteriosus(PDA)and communication between the adjacent parts of the ascending aorta and the pulmonary trunk in 4 patients.Angiocardiographic diagnosis was IAA complicated by APSD in 4 patients.Among them,the right pulmonary artery was found anomalous originating from the ascending aorta.The patient who had IAA(type Ⅰ)with APSD(typeⅡ)and anomalous aortic origin of the right pulmonary artery successfully underwent surgical repair. Conclusion:Angiocardiography is a reliable method in the diagnosis of IAA with APSD.

关 键 词：主动脉弓离断 主-肺动脉间隔缺损 心血管造影 诊断 合并症 

分 类 号：R541.1[医药卫生—心血管疾病] R816.[医药卫生—内科学]