Parkes-Weber综合征的临床及血管造影诊断  

Parkes-Weber Syndrome: Its Clinical and Angiographic Diagnosis

作　　者：杨之晖[1] 华佳[1] 邹爱华[1] 许建荣[1] 徐惊伯[1] 张柏根[2] 

机构地区：[1]上海第二医科大学附属仁济医院放射科,200001 [2]上海第二医科大学附属仁济医院血管外科,200001

出　　处：《临床放射学杂志》2002年第12期968-971,共4页Journal of Clinical Radiology

摘　　要：目的　研究Parkes Weber综合征 (PWS)临床及血管造影特征性表现 ,并进行分析及鉴别。资料与方法　回顾分析 1 7例PWS患者的临床表现及X线平片、动静脉造影及淋巴造影的表现。结果　 1 7例临床主要表现为骨软组织肥大、皮温增高 ,但均无血管杂音及搏动性肿块 ,可伴有皮肤红葡萄色血管瘤及浅静脉曲张 ;平片示骨骼增粗增长 ,软组织肥厚 ;动脉造影表现为患肢动脉干增粗 ,血流加快 ,静脉早期显影 ,而瘘口则不能明确显示 ;1例间接淋巴造影示其淋巴系统明显异常。结论　PWS有其临床及血管造影的特征性表现 。Objective To study the clinical and angiographic manifestations of Parkes Weber syndrome (PWS) and to discuss the diagnosis and differentiation of the disease.Materials and Methods The clinical manifestations and imaging findings, including plain X ray film and arterio , veno as well as lympho graphy, in 17 patients with PWS were retrospectively analyzed.Results Clinically, hypertrophy of the soft tissue and bone and increased skin temperature were the main symptoms. No vascular murmur and pulsatile mass was presented in all cases. Red hemangioma and superficial varicosis were seen in some cases. On plain X ray film, thickened, elongated bone and hypertrophied soft tissue were seen. On angiographs, enlarged main artery with rapid flow and early venous visualization was demonstrated, while the orifice of arteriovenous fistula could not be identified. Obvious lymphatic malformation was revealed on indirect lymphographs in one case.Conclusion Parkes-Weber syndrome carries both clinical and imaging characteristics and it is a separate entity.

关 键 词：Parkes-Weber综合征 动静脉瘘 血管造影 诊断 

分 类 号：R543.5[医药卫生—心血管疾病]