8例骨上皮样血管内皮细胞瘤临床特征与MR表现分析  

Bone Epithelioid Hemangioendothelioma:Clinical Features and MRI in 8 Patients

作　　者：李贝贝[1] 刘静静[1] 任翠萍[1] LI Bei-bei;LIU Jing-jing;REN Cui-ping(Department of MRI,The First Affiliated Hospital of Zhengzhou University,Zhengzhou 450052,Henan Province,China)

机构地区：[1]郑州大学第一附属医院磁共振科,河南郑州450052

出　　处：《中国CT和MRI杂志》2025年第3期194-196,共3页Chinese Journal of CT and MRI

摘　　要：目的探讨骨上皮样血管内皮瘤(B-EHE)的MRI特征性表现及其临床特点。方法对8例(其中女性5例,男性3例)患者的相关临床资料及MRI表现进行回顾性分析。所有患者均经病理证实为骨上皮样血管内皮细胞瘤。8例B-EHE均行MRI检查,其中6例行MRI平扫、动态增强及延迟增强扫描。结果8例B-EHE中,3例位于腰骶椎,2例位于胫骨,1例位于肱骨,1例位于胸骨,1例位于股骨。其中1例合并颅脑上皮样血管内皮瘤,1例合并椎体多发转移灶,其余均为单发。T1WI中,3例病灶呈低信号,5例病灶呈混杂等/低信号。T2WI脂肪抑制序列中,3例呈较均匀高信号,5例呈混杂高信号。8例均可见骨质破坏,4例可见骨膜反应,3例可见软组织肿块形成,6例病变周围软组织可见肿胀,2例伴病理性骨折。肿胀软组织和肿块在T1WI上呈低信号,在T2WI和T2WI脂肪抑制序列呈高信号。6例动态增强扫描中,病变呈强化程度不同,其中1例为轻度强化,1例为中度强化,4例为明显强化。结论B-EHE的MR表现能有效评估病变的范围及性质,需结合临床及病理明确诊断。Objective To investigate the MRI features and clinical characteristics of bone epithelioid hemangioendothelioma(B-EHE).Methods A retrospective analysis was conducted on the relevant clinical data and MRI findings of 8 patients(including 5 females and 3 males).All patients were pathologically confirmed to have bone epithelioid hemangioendothelioma.Results All 8 cases of B-EHE underwent MRI examination,including 6 cases of MRI plain scan,dynamic enhanced scan,and delayed enhanced scan.Among the 8 cases of B-EHE,3 were located in the lumbar sacral vertebrae,2 in the tibia,1 in the humerus,1 in the sternum,and 1 in the femur.One case was complicated with epithelioid hemangioendothelioma of the brain,one case was complicated with multiple metastases of the vertebral body,and the rest were all single lesions.In T1WI,3 lesions showed low signal intensity,and 5 lesions showed mixed equal/low signal intensity.In the T2WI fat suppression sequence,3 cases showed relatively uniform high signal intensity and 5 cases showed mixed high signal intensity.All 8 cases showed bone destruction,4 cases showed periosteal reaction,3 cases showed soft tissue mass formation,6 cases showed swelling of the surrounding soft tissue,and 2 cases had pathological fractures.Swelling soft tissue and masses show low signal on T1WI,and high signal on T2WI and T2WI fat suppression sequences.Among the 6 cases of dynamic contrast-enhanced scans,the lesions showed varying degrees of enhancement,with 1 case showing mild enhancement,1 case showing moderate enhancement,and 4 cases showing significant enhancement.Conclusion The MR manifestations of B-EHE can effectively evaluate the scope and nature of lesions,and a clear diagnosis needs to be made based on clinical and pathological factors.

关 键 词：骨上皮样血管内皮细胞瘤 磁共振成像 增强扫描 骨肿瘤 

分 类 号：R44.52[医药卫生—诊断学]