Improvement in oxygen dynamics after 3 months of home-based respiratory muscle rehabilitation in a patient with complex severe pulmonary hypertension: A case report  

作　　者：Xinxin Yan Ya Song Hongda Zhang Tingting Guo Xin Gao Yan Wu Lu Hua 

机构地区：[1]Department of Cardiology,National Center for Cardiovascular Diseases,Fuwai Hospital,Chinese Academy of Medical Sciences and Peking Union Medical College,Beijing,China [2]Cardiopulmonary Rehabilitation Center,National Center for Cardiovascular Diseases,Fuwai Hospital,Chinese Academy of Medical Sciences and Peking Union Medical College,Beijing,China

出　　处：《Chronic Diseases and Translational Medicine》2025年第1期78-80,共3页慢性疾病与转化医学(英文版)

摘　　要：To the Editor,A 26-year-old woman with congenital heart disease,postatrial septal defect repair,postarterial catheter ligation,hypoxia-associated pulmonary hypertension,and reduced right heart function,which manifested as a severe decrease in activity tolerance,chest tightness and shortness of breath,and easy fatigue of breathing,was treated with oxygen,targeting medications such as anisentan,tadalafil,remodulin,and diuretic potassium supplementation to enhance cardiac function,and then her symptoms were slightly improved compared with the previous ones.She was guided with in-hospital respiratory training to the extent that the patient could tolerate it and then was discharged from the hospital to have a home-based respiratory rehabilitation for a period of 3 months.The training plan was as follows:(i)Respiratory muscle function test:the patient's resting maximal inspiratory pressure(MIP)and maximal expiratory pressure(MEPw)ere assessed by the respiratory trainer equipment,and the respiratory muscle weakness/invulnerability was defined as a measured maximal pressure value less than 80 cmH_(2)0 according to the ERS guidelines.

关 键 词：diuretic potassium supplementation enhance cardiac functionand reduced right heart functionwhich oxygentargeting medications oxygen dynamics home based respiratory muscle rehabilitation complex severe pulmonary hypertension congenital heart diseasepostatrial septal 

分 类 号：R541.6[医药卫生—心血管疾病]