1例“脂肪瘤病”——马德龙病致中心气道狭窄患者行(支)气管镜诊疗操作的麻醉管理  

A case of lipomatosis-anesthetic management of therapeutic bronchoscopy in a patient with tracheal stenosis due to Madrone's disease

作　　者：席鹏 兰杨 卞金俊 杨宇光 Xi Peng;Lan Yang;Bian Jinjun;Yang Yuguang(Department of Anesthesiology,the First Affiliated Hospital of Naval Medical University,Shanghai 200433,China)

机构地区：[1]海军军医大学第一附属医院麻醉科,上海200433

出　　处：《国际麻醉学与复苏杂志》2025年第3期297-300,共4页International Journal of Anesthesiology and Resuscitation

基　　金：围术期气道精细化管理科研项目(RCLX2315006)。

摘　　要：马德龙病也称为良性对称性脂肪瘤病,是一种罕见的疾病,其主要特征是大量脂肪对称性、弥漫性分布于患者颈部周围,常因不美观、运动受限、压迫气管致呼吸困难而就诊,麻醉风险极高。文章报道1例马德龙病致中心气道狭窄拟行急诊(支)气管镜治疗的患者,旨在为该类患者的麻醉管理提供临床参考。Madrone's disease,also known as benign symmetric lipo-matosis,is a rare disease characterized by large amounts of fat tissue symmetrically and diffusely distributed around the patient's neck.Patients seek medical attention mainly for treatment of aesthetic malformations,movement limitation,and dyspnea.It poses a great challenge to anesthetic management.This study reports a case of a patient with central airway stenosis caused by Madrone's disease who was proposed to undergo emergency therapeutic bronchoscopy,aiming to provide a reference for management of this group of patients.

关 键 词：马德龙病 困难气道 (支)气管镜 麻醉管理 经鼻高流量氧疗 

分 类 号：R614[医药卫生—麻醉学]