Marfan’s综合征合并小儿脊柱侧凸的外科治疗探讨  

Treatment of scoliosis associated Marfan's syndrome in children

作　　者：张学军[1] 于凤章[1] 孙琳[1] 李成鑫[1] 祁新宇[1] 潘少川[1] 

机构地区：[1]首都医科大学附属北京儿童医院矫形骨科,100045

出　　处：《中华小儿外科杂志》2003年第1期26-28,共3页Chinese Journal of Pediatric Surgery

摘　　要：目的　探讨Marfan’s综合征合并小儿脊柱畸形的发病机制及治疗原则。方法　 30例Marfan’s综合征合并脊柱畸形的患儿在我院得到矫治及随访。 1 3例采用单纯后路矫形融合 ,1 7例采用前路松解加后路矫形。其中 2 0例曾采用支具等保守疗法。通过对手术前后的顶椎偏移 (AVT) ,顶椎旋转度 (AVR) ,Cobb’s角 ,躯干移位程度 (TS)及身高的变化比较 ,分析总结治疗效果并探讨治疗原则。结果　单纯后路矫形术后并发症较多 ,前后路较大范围的融合疗效较佳。结论　Marfan’s综合征合并小儿脊柱畸形应早期治疗 。Objective To discuss the principle of treatment for scoliosis associated Marfan's syndrome in children.Methods Thirty cases of scoliosis associated Marfan's syndrome were corrected and followed up. Thirteen patients underwent posterior fusion whereas 17 cases received anterior release and pos terior correction. Among the 30 patients, 20 were previously treated with brace and other conservative methods. The results were analyzed using apex vertebral translation (AVT), apex vertebral rotation(AVR), Cobb's angle, trunk shift (TS), and pre and post operative body heights.Results Posterior approach resulted in more complications. Wider range anterior fusion combined with posterior correction improved the results.Conclusion Anterior release combined with posterior correction is the preferred treatment of scoliosis associated Marfan's syndrome.

关 键 词：Marfan's综合征 外科手术 治疗 小儿 脊柱侧凸 

分 类 号：R726.8[医药卫生—儿科]