先天性一侧肺动脉缺如的电子束CT诊断  

Electron beam CT diagnosis of congenital unilateral absence of pulmonary artery

作　　者：周渊[1] 戴汝平[1] 曹程[1] 张戈军[1] 荆宝莲[1] 

机构地区：[1]中国医学科学院中国协和医科大学心血管病研究所阜外心血管病医院放射科,北京100037

出　　处：《中华放射学杂志》2003年第4期311-314,共4页Chinese Journal of Radiology

摘　　要：目的　评价电子束CT(EBCT)诊断先天性一侧肺动脉缺如的价值。方法　对经平片、超声心动图检查后拟诊为肺血管疾病或原发性肺动脉高压的患者行EBCT检查 ,EBCT诊断先天性一侧肺动脉缺如的 11例患者入选 ,并与超声心动图、核素通气灌注扫描、心血管造影的检查结果作进一步的比较及评估。结果　单发一侧肺动脉缺如 4例 ,均为女性成年人。合并多发心血管畸形 7例 ,其中合并复杂畸形 3例 ,均为男性儿童和左肺动脉缺如 ;合并单发心血管畸形 4例 ,其中 3例为右肺动脉缺如。结论　 (1)儿童时期明确诊断的一侧肺动脉缺如多合并有心血管畸形 ,且左肺动脉缺如多见 ,成年人明确诊断的单发一侧肺动脉缺如多为右肺动脉缺如。 (2 )EBCT对先天性一侧肺动脉缺如的诊断有较高的实用价值 ,较之多普勒超声更为准确 ,与心血管造影各具独特优势 。Objective To evaluate the clinical value of electron beam CT (EBCT) in diagnosing congenital unilateral absence of pulmonary artery (UAPA). Methods Patients with clinically suspected pulmonary artery disease or primary pulmonary hypertension underwent EBCT scanning. EBCT confirmed the diagnosis of UAPA in 11 patients, who were also evaluated with echocardiography and chest roentgenography. Cardioangiography and nuclear ventilation perfusion scan were performed in some patients for a comparative study. Results 4 female adults had UAPA without associated congenital anomaly. 3 male children with coexisting complex congenital abnormality had unilateral absence of the left pulmonary artery and 4 patients coexisted other simple cardiovascular anomaly. EBCT scanning simultaneously displayed topographic pattern of both unilateral absence of pulmonary artery and coexisting congenital cardiovascular anomaly, as well as lung diseases. Conclusion UAPA diagnosed in childhood usually has unilateral absence of the left pulmonary artery and associated congenital cardiovascular anomaly, while UAPA diagnosed in adult usually has UAPA on the right side without associated congenital anomaly. EBCT is one of the optimal imaging techniques in diagnosing UAPA and it greatly increases the diagnostic efficacy than echocardiography dose. Both EBCT and cardioangiography have their own advantages, however, EBCT, as a noninvasive method, should be complementary and not exclusive.

关 键 词：先天性一侧肺动脉缺如 电子束CT诊断 超声心动图 核素通气灌注扫描 心血管造影 

分 类 号：R816.41[医药卫生—放射医学]