法乐氏四联症的外科治疗34例分析  

Study of surgical management of 34 case of tetralogy of fallot

作　　者：梁葳[1] 李韬[1] 周其文[1] 杨东山[1] 

机构地区：[1]广东省茂名市人民医院心胸外科,广东茂名525000

出　　处：《河北医学》2004年第3期239-242,共4页Hebei Medicine

摘　　要：目的 :总结法乐氏四联症外科治疗经验。方法 :共 34例 ,年龄 2～ 1 6岁 ,32例在中低温体外循环、胸部正中切口行法乐氏四联症根治术 ,1例在非体外循环下行改良B -T分流术 ,1例行根治术同时行双向Glenn分流术。结果 :术后早期死亡 1例 ,死亡原因为低心排综合征 ,无远期死亡。结论 :本症应争取早日行根治术 ,肺动脉发育差者应行改良B -T分流术 ,右室发育不良者在行根治术同时行双向Glenn分流术 ,死亡原因以低心排综合征多见 ,应采取合适的手术方式及围术期多种方法预防。Objective: To report the experience of surgical intervention for tetralogy of fallot(TOF). Method: A total of 34 patients with TOF,age 2～16 years,32 patients received the complete repair through mediam sternotomy under Moderate-hypothermic cardiopulmonary bypass.1 patient received modified Blalock-Taussing shunt without cardiopulmonary bypass,1 TOF patient with right ventricle severe hypoplasia received bidirectional Glenn shunt and complete repair.Results:One patient died of low cardiac output syndrome(LOS)in early postoperative period,noneof them died in later period.Conclusion:The complete repair of TOF should be performed as early as possible, TOF with pulmonary arterial hypoplasia should received modified Blalock-Taussing shunt,TOF with right ventricle severe hypoplasia should received bi-directional Glenn shunt and complete repair.The main cause of death is low cardiac output syndrome,it should be prevent by appropriate cardiac surgical procedures and other multiple therapies in perioperative period.

关 键 词：法乐氏四联症 心脏外科手术 低心排综合征 

分 类 号：R726.5[医药卫生—儿科]