Herlyn-Werner-Wunderlich Syndrome Presenting with Abdominal Pain: A Case Report  

作　　者：Hayat Al-Jumah Rashida Sadiq Noor Al-Muslem Fathia E. Al-Jama Raghad Aljishi Salah Abohelaika Hayat Al-Jumah;Rashida Sadiq;Noor Al-Muslem;Fathia E. Al-Jama;Raghad Aljishi;Salah Abohelaika(Department of Obstetrics and Gynecology, Qatif Central Hosptial, Qatif, KSA;Department of Radiology, Qatif Central Hosptial, Qatif, KSA;King Fahad University Hospital, Private Health Services Centre, Khobar, KSA;Royal College of Surgeons, Dublin, Ireland;Clinical Pharmacology Department, Qatif Central Hosptial, Qatif, KSA)

机构地区：[1]Department of Obstetrics and Gynecology, Qatif Central Hosptial, Qatif, KSA [2]Department of Radiology, Qatif Central Hosptial, Qatif, KSA [3]King Fahad University Hospital, Private Health Services Centre, Khobar, KSA [4]Royal College of Surgeons, Dublin, Ireland [5]Clinical Pharmacology Department, Qatif Central Hosptial, Qatif, KSA

出　　处：《Open Journal of Obstetrics and Gynecology》2021年第7期911-916,共6页妇产科期刊（英文）

摘　　要：Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital anomaly characterized by <span style="font-family:Verdana;">triad</span><span style="font-family:Verdana;"> of uterus didelphys, obstructed </span><span style="font-family:Verdana;">hemi</span><span style="font-family:Verdana;"> vagina, and ipsilateral renal agenesis. The most common presentation is abdominal pain, dysmenorrhea, and abdominal mass secondary to </span><span style="font-family:Verdana;">hemi</span><span style="font-family:Verdana;">-</span><span style="font-family:Verdana;">hematometrocolpos</span><span style="font-family:Verdana;">. We report an emergency presentation of this syndrome during the pandemic of COVID-19 in Qatif Central Hospital, Saudi Arabia, April 2020. An 11-year-old Saudi girl presented to the emergency room with three months history of cyclical lower abdominal pain. The pain was progressive, continuous </span><span style="font-family:Verdana;">and</span><span style="font-family:Verdana;"> not relieved by analgesics. Abdominal examination revealed a tender abdominal mass mainly in the left iliac fossa, Ultrasound evaluation showed two uterine bodies. The left uterus was distended with complex fluid. Pelvic MRI findings consistent with Herlyn-Werner-Wunderlich (HWW) syndrome were found with uterine </span><span style="font-family:Verdana;">didelphys</span><span style="font-family:Verdana;"> and </span><span style="font-family:Verdana;">left sided</span><span style="font-family:Verdana;"> hematometra resulting from obstructed </span><span style="font-family:Verdana;">hemi</span><span style="font-family:Verdana;">-vagina and ipsilateral agenesis of the left kidney. Resection of the vaginal septum and drainage of hematometra was done. The patient recovered with normal cyclical menstruation. Cyclical or continuous lower abdominal pain with or without amenorrhea is the usual presentation of HWW syndrome during adolescence. Diagnosis is made by ultrasonography and MRI. Early diagnosis and accurate management can provide pain reHerlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital anomaly characterized by <span style="font-family:Verdana;">triad</span><span style="font-family:Verdana;"> of uterus didelphys, obstructed </span><span style="font-family:Verdana;">hemi</span><span style="font-family:Verdana;"> vagina, and ipsilateral renal agenesis. The most common presentation is abdominal pain, dysmenorrhea, and abdominal mass secondary to </span><span style="font-family:Verdana;">hemi</span><span style="font-family:Verdana;">-</span><span style="font-family:Verdana;">hematometrocolpos</span><span style="font-family:Verdana;">. We report an emergency presentation of this syndrome during the pandemic of COVID-19 in Qatif Central Hospital, Saudi Arabia, April 2020. An 11-year-old Saudi girl presented to the emergency room with three months history of cyclical lower abdominal pain. The pain was progressive, continuous </span><span style="font-family:Verdana;">and</span><span style="font-family:Verdana;"> not relieved by analgesics. Abdominal examination revealed a tender abdominal mass mainly in the left iliac fossa, Ultrasound evaluation showed two uterine bodies. The left uterus was distended with complex fluid. Pelvic MRI findings consistent with Herlyn-Werner-Wunderlich (HWW) syndrome were found with uterine </span><span style="font-family:Verdana;">didelphys</span><span style="font-family:Verdana;"> and </span><span style="font-family:Verdana;">left sided</span><span style="font-family:Verdana;"> hematometra resulting from obstructed </span><span style="font-family:Verdana;">hemi</span><span style="font-family:Verdana;">-vagina and ipsilateral agenesis of the left kidney. Resection of the vaginal septum and drainage of hematometra was done. The patient recovered with normal cyclical menstruation. Cyclical or continuous lower abdominal pain with or without amenorrhea is the usual presentation of HWW syndrome during adolescence. Diagnosis is made by ultrasonography and MRI. Early diagnosis and accurate management can provide pain re

关 键 词：Herlyn-Werner-Wunderlich Syndrome Obstructed Hemi-Vagina Hematometrocolpos Mullerian Anomaly VAGINOPLASTY 

分 类 号：R24[医药卫生—中医临床基础]