Ebstein Anomaly: A Clinical Case Series among Adolescents in Guinea  

作　　者：Mamadou Bassirou Bah Elhadj Yaya Baldé Mamadou Aliou Baldé Thierno Siradjo Baldé Mariama Djalakhan Diallo Amadou Diouldé Doumbouya Ibrahima Sory Sylla Alpha Koné Ibrahima Sory Barry Souleymane Diakité Sana Samoura Mamadou Diallo Abdoulaye Camara Mamadou Dadhi Baldé Mamadou Bassirou Bah;Elhadj Yaya Baldé;Mamadou Aliou Baldé;Thierno Siradjo Baldé;Mariama Djalakhan Diallo;Amadou Diouldé Doumbouya;Ibrahima Sory Sylla;Alpha Koné;Ibrahima Sory Barry;Souleymane Diakité;Sana Samoura;Mamadou Diallo;Abdoulaye Camara;Mamadou Dadhi Baldé(Cardiology Department, Ignace Deen Hospital, Conakry, Guinea;Cardiology Department, Donka Hospital, Conakry, Guinea)

机构地区：[1]Cardiology Department, Ignace Deen Hospital, Conakry, Guinea [2]Cardiology Department, Donka Hospital, Conakry, Guinea

出　　处：《World Journal of Cardiovascular Diseases》2023年第4期228-235,共8页心血管病（英文）

摘　　要：Ebstein’s anomaly is a rare congenital heart disease. We report a series of 4 cases of Ebstein’s anomaly discovered in adolescents. The mean age was 13.75 ± 0.96, with 3 boys and one girl. Three were in heart failure. The EKG showed atrial hypertrophy (1 case), right bundle branch block (1 case), Wolff-Parkinson-White (1 case), and atrial fibrillation (1 case). Cardiomegaly was present in all patients with a mean cardiothoracic index of 0.77 ± 0.03. On echocardiography, the mean apical displacement of the tricuspid septal leaflet was 22.5 ± 3.30 mm/m², the Celermajer index was Grade 2 in 2 patients and Grade 4 in 2 patients. Depletive medical treatment was prescribed to 3 patients. Anticoagulant therapy was initiated in one patient. Two are awaiting surgery. One death was recorded, it was at Grade 4 of the Celermajer index.Ebstein’s anomaly is a rare congenital heart disease. We report a series of 4 cases of Ebstein’s anomaly discovered in adolescents. The mean age was 13.75 ± 0.96, with 3 boys and one girl. Three were in heart failure. The EKG showed atrial hypertrophy (1 case), right bundle branch block (1 case), Wolff-Parkinson-White (1 case), and atrial fibrillation (1 case). Cardiomegaly was present in all patients with a mean cardiothoracic index of 0.77 ± 0.03. On echocardiography, the mean apical displacement of the tricuspid septal leaflet was 22.5 ± 3.30 mm/m², the Celermajer index was Grade 2 in 2 patients and Grade 4 in 2 patients. Depletive medical treatment was prescribed to 3 patients. Anticoagulant therapy was initiated in one patient. Two are awaiting surgery. One death was recorded, it was at Grade 4 of the Celermajer index.

关 键 词：Ebstein Anomaly ADOLESCENT Congenital Heart Disease GUINEA 

分 类 号：R54[医药卫生—心血管疾病]