彩色多普勒超声检测肝豆状核变性的肝脏改变  被引量:1

Changes of the color Doppler ultrasonic imaging in patients with HLD

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作  者:虞梅 刘康永 王骊 钦晨 何海萍 钱武凌 王慧 曹亮 李顺钧 施利华 

机构地区:[1]上海大华医院超声室脑病中心,200237

出  处:《上海医学影像》2004年第3期197-199,共3页Shanghai Medical Imaging

摘  要:目的 通过分析肝豆状核变性(hepatolenticular degeneration HLD)的超声征象及其病理变化与临床表现提高对HLD病的认识及诊断的正确率。方法 全部36例均行彩色多普勒超声检查,回顾性分析其病理变化及临床表现。结果 彩色多普勒超声提示全部病例都有不同程度的肝损害图像及门静脉血流参数的改变。大致可分为四型:Ⅰ型.弥漫性点状增强型:16例表现肝区光点弥漫性点状增强回声;Ⅱ型.光点不均匀增粗型:12例呈肝光点不均匀增粗型硬化;Ⅲ型.小结节型:5例呈肝区光点呈小结节型硬化:Ⅳ型.大结节与小结节并存型:3例声像图表现为肝区大结节与小结节并存,间隔类似肝癌的团块状回声。根据超声不同的表现均有不同程度的门静脉血流动力学改变。大结节型与小结节型的肝硬化门静脉血流明显降低。结论 肝豆状核性变声像图最多表现为肝区光点弥漫性点状增强及肝光点不均匀增粗型。特别是肝区弥漫性点状增强回声最具特征性。Objective the echographic changes of liver in patients with hepatolenticular degeneration (HLD). Methods Thirty six patients with HLD had color Doppler ultrasonographic study on their liver and blood index of portal vein. Results The ultrasonic features of liver and blood of portal vein in all patients with HLD had certain abnormal changes to different extent. The ultrasonic changes of liver can be divided into four types: 1.Diffuse spotty enhanced type(16 cases);2.Spotty inhonopeneously widened type(12 cases);3.Small nodule type(5 cases); 4.Greater tubercle combined with nodule type (3 cases). The ultrasonic changes of blood of portal vein had the most distinct decrease in greater tubercle combined with nodule type patients. Conclusion Diffuse spotty enhanced type and spotty widened type are the most common ultrasonic changes in patients with HLD, and especially diffuse spotty enhanced type is the most characteristic change.

关 键 词:彩色多普勒超声 超声检测 肝豆状核变性 诊断 肝脏改变 超声征象 

分 类 号:R742.4[医药卫生—神经病学与精神病学] R445.1[医药卫生—临床医学]

 

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