肾错构瘤合并结节性硬化的诊断与治疗(4例报告与文献复习)  

The Diagnosis and Management of Renal Angiomyolipoma Associated with Tuberous Sclerosis

作　　者：唐雪鸿[1] 高旭[1] 孙颖浩[1] 

机构地区：[1]解放军第二军医大学附属长海医院泌尿外科,上海200433

出　　处：《临床军医杂志》2005年第1期63-65,共3页Clinical Journal of Medical Officers

摘　　要：目的　进一步提高对肾错构瘤合并结节性硬化的诊断和治疗水平。方法　对 4例肾错构瘤合并结节性硬化患者的临床资料和随访情况进行回顾性分析。结果　4例肾错构瘤合并结节性硬化患者均行手术治疗,术后病理结果明确诊断,术后定期复查B超,平均随访 30个月,均无复发。结论　肾错构瘤合并结节性硬化的患者多为双侧多发性病变,如一定要行手术治疗应慎重,必须要考虑肾功能的保留问题,肾部分切除和或选择性肾动脉栓塞术为首选。Objective To evaluate the diagnosis and the management of renal angiomyolipoma associated with tuberous sclerosis. Methods Four cases of renal angiomyolipoma associated with tuberous sclerosis treated from 1998 to 2004 were analyzed retrospectively.Results The four cases were treated by operation, and the diagnosis was confirmed via postoperatively pathological findings. The therapeutic results were satisfactory and no relapse was found in mean 30 months' follow-up. Conclusion Renal preservation should be given proper consideration if surgical management is necessary, for bilaterally multiple lesions are common in the patients with renal angiomyolipoma associated with tuberous sclerosis. Partial nephrectomy and selective renal arterial embolization under angiography are the first choices.

关 键 词：肾错构瘤 结节性硬化 

分 类 号：R737.11[医药卫生—肿瘤]