鞍区副神经节瘤的MR诊断——附1例报告及文献复习  

MR findings of paragangliomas of the parasellar region:one case report and review of literature

作　　者：罗萍[1] 李坤成[1] 杨小平[1] 孙燕妮[2] 

机构地区：[1]首都医科大学宣武医院放射科,北京100053 [2]首都医科大学宣武医院病理科

出　　处：《罕少疾病杂志》2005年第2期12-14,17,共4页Journal of Rare and Uncommon Diseases

摘　　要：目的探讨原发于鞍区的副神经节瘤的MR诊断及相关的病理、组织学起源。方法回顾性分析我院收治的1例鞍区副神经节瘤的临床资料,并进行文献复习。结果患儿,男性,5周岁,以生长发育迟缓就诊。MR检查发现鞍区有实性占位,边界清晰,明显均匀强化。病理证实为副神经节瘤。结论鞍区副神经节瘤系罕见肿瘤。“椒盐征”为其典型MR表现。但瘤体较小,表现不典型时应与发生于鞍区的其它实质性肿瘤相鉴别。MR检查对发生于头颈部的副神经节瘤的诊断具有很大价值。Objective To study the MR findings of primary intrasellar and suprasellar paragangliomas, pathological features and possible origin. Methods The clinical datum of 1 patient with paragangliomas of the parasellar region was analyzed retrospectively and the literature was reviewed. Results A five-year-old boy had suffered from growth retardation for two years. Magnetic resonance imaging showed an intra- and suprasellar mass which compressed the optic chiasm lightly. The lesion was homogeneous and gave the iso-density siginal on T1 and T2-weighted images. The margin was sharp. Gadolinium administration produced strong homogeneous enhancement. The pathological examination revealed primary paraganglioma. Conclusion Paraganglioma is very rare in the sellar area, where there are normally no paragangliomic cells. In larger lesions, the “salt-and-pepper” appearances on T2-weighted images are characteristics of paragangliomas. It should be differentiated from other parenchymatous tumor in the parasellar region if paraganglioma is not typical. MR imaging can provide essential informations for diagnosis of the patients with paragangliomas.

关 键 词：副神经节瘤 化学感受器瘤 鞍区肿瘤 磁共振成像 

分 类 号：R739.41[医药卫生—肿瘤]