结节性硬化症的CT和MRI诊断  

CT and MRI Diagnosis of Tuberous Sclerosis

作　　者：吴耀贤 孔祥泉[2] 刘晓斌 高兴军 

机构地区：[1]河南省信阳市中心医院影像科,464000 [2]华中科技大学同济医学院附属协和医院放射科,武汉430022 [3]河南省息县县医院放射科,464300

出　　处：《临床放射学杂志》2005年第6期478-480,共3页Journal of Clinical Radiology

摘　　要：目的分析结节性硬化(TS)的CT和MRI表现特征,提出TS的影像学分型。资料与方法回顾性分析28例经临床和手术确诊的TS患者影像学资料,根据脑内钙化或非钙化结节的位置及是否合并脑内或其他脏器病变进行影像学分型。结果Ⅰ型8例,结节主要分布于侧脑室室管膜下;Ⅱa型9例,结节分布于室管膜下和大脑皮层,Ⅱb型7例,结节分布于室管膜下和白质区;Ⅲ型4例,其中2例合并肾脏错构瘤,1例合并脑内巨细胞星形细胞瘤,1例合并小脑蚓部血管畸形。结论对TS进行影像学分型是必要的,影像学发现的结节位置及合并症是TS预后的决定因素。Objective To analyze CT and MRI characteristic features of tuberous sclerosis (TS) and propose the imaging classification of TS.Materials and Methods 28 patients with tuberous sclerosis proved by clinic and operation data were reviewed retrospectively. The location of calcification or intracranial noncalcification nodules and complications in other organs were recorded to classify.Results Type Ⅰ: 8 patients with isolated subependymal nodules. Type Ⅱa: 9 patients had cortical tubers associated with subependymal nodules. Type Ⅱb: 7 patients had white matter lesions associated with subependymal nodules. Type Ⅲ: 2 patients with renal hamartoma, 1 patient with subependymal giant cell astrocytoma, 1 patient with cerebellar arteriovenous malformations.Conclusion It is necessary to classify the imaging features of TS, the location of nodules and complications are key factors for the prognosis of TS.

关 键 词：结节性硬化症 MRI诊断 CT 影像学分型 室管膜下 影像学资料 回顾性分析 肾脏错构瘤 星形细胞瘤 表现特征 脏器病变 钙化结节 脑内钙化 大脑皮层 血管畸形 小脑蚓部 决定因素 侧脑室 分布 Ⅱa型 Ⅱb型 巨细胞 合并症 

分 类 号：R445[医药卫生—影像医学与核医学]