偏侧萎缩-偏侧帕金森综合征——6例报道并文献复习  

Hemiatrophy-Hemiparkinsonism Syndrome:a report of 6 cases and Review of the literature

作　　者：陈斐[1] 曹建淳[1] 

机构地区：[1]上海铁道大学医学院附属甘泉医院神经内科,200065

出　　处：《罕少疾病杂志》2000年第4期8-9,共2页Journal of Rare and Uncommon Diseases

摘　　要：目的通过分析 6例偏侧萎缩－偏侧帕金森综合征 (HAHP)的临床资料，探讨 HAHP的病因，临床表现，诊断和治疗。方法对 6例 HAHP病人的临床表现进行详细分析并综合文献报告。结果 6例病人全部符合 Bushman等 1988年提出的 HA诊断标准，其中 5例确诊， 1例拟诊。 2例疑诊 HAHP。 6例病人都接受了 B族维生素、地巴唑、胞二磷胆碱、安坦等药物治疗，但几无疗效。结论 HAHP是一种罕见的临床综合征，病因不明。临床上主要表现为偏侧萎缩、偏侧帕金森综合征、发作性肌张力障碍。 HAHP的诊断主要依靠临床表现，神经影像资料可能有助诊断。迄今， HAHP尚无有效治疗。Objective To explore the etiology,clinical feature,diagnosis and treatment of hemiatrophy－ hemiparkinsonism syndrome(HAHP).Methods The clinical data of 6 patients with HAHP were studied and literature about the disease were reviewed.Results The diagnoses of 6 patients were all met with the criteria of HA by Bushman in 1988.5 of 6 cases were definite HA,1 of 6 cases was probable HA.However,only 2 of 6 were possible HAHP.All patients were prescribed vitamin B,dibazol,cilicoline,antane,and so on.But,the effect of these drugs were poor.Conclusion HAHP is a rare clinical syndrome.It is characterized by hemiatrophy,hemiparkinsonism and paroxysmal dystonia.The diagnosis is dependent on its clinical feature.Neuroimage may be helpful for the diagnosis.There is no effective treatment for it.

关 键 词：偏侧萎缩-偏侧帕金森综合征 临床表现 诊断 治疗 

分 类 号：R742[医药卫生—神经病学与精神病学]