听神经病小儿60例分析  

Analysis of 60 children with auditory neuropathy

作　　者：曾咏梅[1] 朱雅颖[1] 顾文琇[1] 

机构地区：[1]上海复旦大学附属眼耳鼻喉医院耳科,上海200031

出　　处：《中国听力语言康复科学杂志》2006年第2期28-31,共4页Chinese Scientific Journal of Hearing and Speech Rehabilitation

摘　　要：目的对60例听神经病小儿进行临床听力学分析,以便提高对此病的认识,避免漏诊及误诊。方法2003年-2005年我院临床医学听觉言语康复中心门诊,对4个月-6岁婴幼儿及儿童诊疗中发现60例聋儿,对声音有反应,但不会讲话,给于ABR、ASSR、OAE、声导抗、影像学检查后,发现异常反应。结果60例(120耳)聋儿ABR严重异常,ASSR、行为测听有部分残余听力、OAE正常、声导抗及影像学方面未发现异常。结论听神经病是一种近期提出的病因不明的听觉障碍性疾病。此病引起具有特殊临床表现与听力学检查表现的感音神经性聋,有助于与感音性聋的鉴别。Objective To improve the identification of auditory neuropathy in children and avoid underestimation or improper diagnosises. Method From 2003 to 2005,60 children （4 month to 6 years） from the outpatient wards of our medical center were selected because they showed hearing but could not speak. They were tested by auditory brainstem response （ABR）, auditory steady-state response （ASSR）, otoacoustic emissions （OAE）, audiometry, acoustic impedance and imaging. Results The results indicated that 60 children （120 ears） showed significantly abnormal ABR, but had residual hearing in ASSR and audiometry, normal OAE, acoustic impedance and imaging. Conclusion Auditory neuropathy was an idiopathic disease with hearing impairment. It had special clinical manifestations and audiometric characteristics distinguished from other common sensorineural hearing loss. More attention should be paid during diagnosis to improve the identification of auditory neuropathy.

关 键 词：听神经病 听性脑干反应 多频稳态反应 耳声发射 聋儿 

分 类 号：R764.4[医药卫生—耳鼻咽喉科]