下丘脑神经元错构瘤临床及MRI表现  

CLINICAL AND MRI CHARACTERISTICS OF HYPOTHALAMIC NEURONAL HAMARTOMA

作　　者：万衡[1] 张倩[2] 杨跃林[1] 韩俗[1] 邝璞[3] 魏鑫[3] 

机构地区：[1]四川大学华西第四医院,成都610041 [2]四川(西藏)华西普济医院 [3]四川大学华西医院

出　　处：《现代预防医学》2007年第9期1624-1626,共3页Modern Preventive Medicine

摘　　要：[目的]研究下丘脑神经元错构瘤的临床特点及MRI(磁共振成像)表现。[方法]分析了经临床及MRI共同诊断的下丘脑神经元错构瘤8例的特征。[结果]T1像上错构瘤均表现为均匀等信号团块,T2像上肿块与脑灰质信号相似。肿块以广基底或窄基底广基与灰结节和乳头体相连。[结论]当患儿出现性早熟和(或)痴笑样癫痫为主的临床表现时,MRI显示灰结节和乳头体球形样肿块时,应首先考虑本病。[Objective] To study the MRI （magnetic resonance imaging） findings of the hypothalamic neuronal hamartoma and its clinical characteristic. [Methods] The characteristics of 8 patients underwent MRI plain scan and enhaocement scanning were analyzed. [ Results] In MRI plain scan imagings, the hypothalamic neuronal hamartomas shinned as isointense masses on T1WI, while it showed similar with the ectocinerea on T2WI. No enhancement was founded. The hypothalamic neuronal hamartomas connected to gray tubercle and bulla of fornix with wide or narrow base. [Conclusion] When patients have the symptom of gelastic epilepsy and/or precocious puberty, and MRI scan imagings show masses connected to gray tubercle and bulla of fornix, the hypothalamic neuronal hamartoma needs to be considered firstly.

关 键 词：下丘脑错构瘤 性早熟 MRI 

分 类 号：R742.89[医药卫生—神经病学与精神病学]