双肾多发性错构瘤合并结节性硬化的诊断治疗  

Diagnosis and management of bilateral and multifocal renal angiomyolipomas associated with tuberous sclerosis

作　　者：王养民[1] 刘尚文[1] 周大海[1] 周逢海[1] 

机构地区：[1]兰州军区兰州总医院全军泌尿外科中心,甘肃兰州730050

出　　处：《西北国防医学杂志》2007年第4期268-269,共2页Medical Journal of National Defending Forces in Northwest China

摘　　要：目的:提高双肾多发性错构瘤合并结节性硬化的诊断与治疗水平。方法:对4例双肾多发性错构瘤合并结节性硬化患者的临床资料和随访情况进行回顾性分析。结果:1例接受单侧肾切除手术治疗,术后10 d死于多器官功能衰竭;1例行肿瘤剜除术,术后恢复良好;2例随访24个月病情无进展。结论:双肾多发性错构瘤合并结节性硬化患者在无症状期,应严密观察;手术治疗应慎重,症状进展较快时,肿瘤剜除术为首选。Objective： To evaluate the diagnosis and management of bilateral and muhifocal renal angiomyolipomas associated with tuberous sclerosis. Methods： The clinical data from 4 patients with bilateral and muhifocal renal angiomyolipomas associated with tuberous sclerosis were analyzed retrospectively. Results： l of the 4 patients who had undergone nephrectomy died of multiple organ failure, another patient received successfully renal- sparing surgery. The other two patients were treated conservatively and followed up for twenty -four months. Conclusion： Being in the asymptomatic stage, the patients with bilateral and muhifocal renal angiomyolipomas associated with tuberous sclerosis can be managed conservatively and examined by computerized tomography. Selective renal -sparing surgery may be the first choice of intervention in patients with rapid development of symptoms.

关 键 词：双肾多发性错构瘤 结节性硬化 肿瘤 治疗 

分 类 号：R737.11[医药卫生—肿瘤]