Rhabdoid Meningioma in a Child:Report of a Case and Literatures Review  

儿童横纹肌样脑膜瘤:附病例报告及文献分析(英文)

作　　者：蔡春泉 张庆江 申长虹 杨卫东 胡晓丽 王春祥 马骁 侯志彬 

机构地区：[1]天津儿童医院神经外科 [2]Department of Pediatric Neurosurgery,Tian- jin Children’s Hospital [3]Department of Pathology,Tianjin Children’s Hospital [4]Department of Radiology,Tianjin Children’s Hospital

出　　处：《Chinese Journal of Clinical Oncology》2008年第1期67-71,共5页中国肿瘤临床（英文版）

摘　　要：Meningiomas occur in 1%-4% of primary intracranial tumors in the pediatric group, and is increasing in incidence with age. Some authors have reported that meningioma is more prevalent among adult males, but there is no gender prevalence. The accepted origin of meningiomas is from the arachnoid ceils lining the meninges, or the choroid plexuses. Since Beckwith and Palmer introduced the term ＇rhabdoid tumor＇ in 1978 in reference to a subgroup of childhood malignant renal tumors, many tumors with a rhabdoid morphology have been reported in various sites, including the central nervous system. In 1998 Kepes et al.儿童横纹肌样脑膜瘤是近年来报道的一种很少见的高度恶性肿瘤,具有易复发、病程进展迅速的特点,2000年WHO神经系统肿瘤的分类中,将其作为脑膜瘤的一个新的组织学变型而列出来(Ⅲ级)。笔者报道一例以头痛、呕吐伴抽搐为主要症状的该症患儿,其头颅CT表现为左额叶略高密度肿物,造影剂增强扫描后该肿物明显强化。全麻下行肿物切除术,术后病理诊断为横纹肌样脑膜瘤。术中、术后患儿病情平稳,该患儿及家属拒绝进一步治疗。目前,患儿随访2.5年未见复发征象。本文在回顾性分析该例患儿临床、影像及病理资料同时结合文献讨论了儿童横纹肌样脑膜瘤的诊断及治疗特点,以期提高对该病的认识。

关 键 词：MENINGIOMA RHABDOID DIAGNOSIS immunohistochemical staining. 

分 类 号：R739.4[医药卫生—肿瘤]