苗勒管永存综合征(2例报告并文献复习)  

Persistent Müllerian Duct Syndrome:A Report of 2 Cases and Review of the Literature

作　　者：居小兵[1] 张炜[1] 吴宏飞[1] 钱立新[1] 沈百欣[1] 徐正铨[1] 眭元庚[1] 

机构地区：[1]南京医科大学第一附属医院泌尿外科,江苏南京210029

出　　处：《中华男科学杂志》2008年第1期51-54,共4页National Journal of Andrology

摘　　要：目的：探讨苗勒管永存综合征（PMDS）的病因、临床表现、诊断和治疗。方法：报告2例PMDS。1例伴睾丸横过异位；另1例伴隐睾。伴隐睾者予隐睾切除，两者均接受子宫体大部切除和睾丸固定术。结果：随访1.5-2年，2例患者睾丸质地、血流均正常。结论：PMDS为一种男性假两性畸形，治疗应力求保护睾丸的血供和生殖功能，并密切随访。Objective： To study the etiopathogenesis, clinical manifestations, diagnosis and management of persistent Mǚllerian duct syndrome （PMDS）. Methods： Two cases of PMDS were reported, one accompanied by transverse testicular ectopia and the other associated with cryptorchidism. Corporeal hysterectomy and orchidopexy were given to both the patients and cryptorchidectory the latter. Results ： Vascular supply and texture of the testis were normal in both the 2 patients after 1.5-2 years＇ follow-up. Conclusion： PMDS is male pseudohermaphroditism, for which means should be taken to preserve the blood supply and fertility function of the testis in surgical management, and attention should be paid to possible development of testis tumor in follow-up.

关 键 词：假两性畸形 苗勒管永存综合征 苗勒管抑制激素 男性 

分 类 号：R691.1[医药卫生—泌尿科学]