Sturge-Weber综合征的CT和MRI诊断(附9例报告)  

Diagnosis of SturgeWeber Syndrome on CT and MRI: Report of 9 Cases

作　　者：肖家和[1] 王大有[1] 邓开鸿[1] 

机构地区：[1]华西医科大学附一院放射科

出　　处：《临床放射学杂志》1998年第2期72-74,共3页Journal of Clinical Radiology

摘　　要：目的：研究Ｓｔｕｒｇｅ－Ｗｅｂｅｒ综合征的ＣＴ、ＭＲＩ表现特点，并评价两种检查方法的诊断价值。材料与方法：回顾分析９例Ｓｔｕｒｇｅ－Ｗｅｂｅｒ综合征的临床及影像学资料。全部病例均有面部三叉神经分布区皮肤血管瘤以及同侧颅内相关的病理改变。经ＣＴ检查６例，ＭＲＩ检查３例。结果：ＣＴ、ＭＲＩ显示患侧皮层钙化９例，脑萎缩７例，侧室脉络丛增大３例，颅盖板障增厚５例。增强ＣＴ显示脉络丛明显强化２例，钙化灶周围脑回状强化１例。ＭＲＩ显示侧室脉络丛增大及室管膜下静脉扩张１例。结论：ＣＴ和ＭＲＩ能有效地发现Ｓｔｕｒｇｅ－Ｗｅｂｅｒ综合征的颅内病理改变。在显示皮层钙化灶的存在和范围上，ＣＴ优于ＭＲＩ。但在显示脑实质的其他异常，软脑膜血管瘤畸形和伴发的血管性异常方面，ＭＲＩ则优于ＣＴ。Objective: To study CT and MR imaging manifestations of SturgeWeber syndrome, and evaluate diagnostic value of both imaging methods for this disease.Materials and Methods:The clinical information and imaging findings of 9 patients with SturgeWeber syndrome were analysed retrospectively. In all patients, facial nerves involving region of trigeminal nerve and intracranial abnormalities ipsilateral to facial lesion were found. 6 patients were examined with CT, and 3 patients with MR imaging.Results:On the affected hemisphere, cortical calcifications (n=9), brain atrophy (n=7), choroid plexus enlargement of lateral ventricles (n=3) and cranial diploetic prominence (n=5) were demonstrated by CT or MRI. On postcontrast CT, prominent enhancement of choroid plexus was observed in 2 cases, and gyriform enhancement in the surrounding parenchyma of cortical calcifications occured in one case. On MRI, dilated subependymal veins and prominent choroid plexus were seen simultaneously in one case. Conclusion: CT and MRI can effectively demonstrate intracranial abnormalities of SturgeWeber syndrome. CT was better than MRI in detecting the presence and extent of cortical calcifications, MRI was better than CT in exhibiting brain parenchymal abnormalities, leptomeningeal angiomatous malformation and associated vascular abnormalities. 

关 键 词：S-W综合征 CT 磁共振成像 血管瘤 

分 类 号：R732.2[医药卫生—肿瘤]