一家系多发血管脂肪瘤的临床病理研究  

THE CLINICOPATHOLOGICAL STUDY OF MULTIPLE ANGIOLIPOMA IN ONE FAMILY

作　　者：王海燕[1] 薛明明[2] 王建忠[1] 侯二飞[1] 许贵存[3] 

机构地区：[1]内蒙古医学院基础医学院人体解剖学教研室,内蒙古呼和浩特010059 [2]内蒙古医学院基础医学院生理教研室 [3]内蒙古医学院附属医院

出　　处：《内蒙古医学院学报》2010年第2期117-120,共4页Acta Academiae Medicinae Neimongol

基　　金：内蒙古自治区自然科学基金(200607010914)

摘　　要：目的：观察一家系中血管脂肪瘤病人的临床病理特征。方法：该家系成员共102人,逐个进行临床体检,对9名病人手术切取其中1~2枚肿瘤行病理检查。结果：9名病人具有非常相似的临床特征,即成年后发病,病变为四肢躯干体表对称分布,多个质中等偏软、界清、无痛的圆形,椭圆形或扁块状软组织肿块,活动度好,有明显的遗传特性,病理诊断均为血管脂肪瘤。结论：血管脂肪瘤是一种具有遗传特性的疾病,成年后发病,表现为四肢、躯干对性分布的多个大小不等的皮下软组织肿块,质中等偏软、无痛、界清、活动度良好,其病理特征为由成熟的脂肪细胞和增生的毛细血管构成,有包膜,可见纤维蛋白性血栓形成。Objective：To observe the clinicopathological features of multiple angiolipoma in one family in detail.Methods：Physical examinations were done for 102 persons in this family.The clinicopathological features of 1 or 2 tumor cut from nine patients were examined.Results：Nine patients have similar clinical manifestation which came down with the illness after adults,and had a few tumors in the soft tissue on the whole body,mediam quantity,boundary line,round alike,good activity and obvious heredity.All of them belong to angiolipoma on the pathological diagnosis.Conclusion：Angiolipoma is a heredity which comes down with the illness after adults.Many tumors are scattered in soft tissue of the trunk and the limbs.All tumors are mediam quantity,boundary line,painless,good activity.The pathology consists of mature fat cell and hyperplastic capillary.The tumor has membrane and fibrinous thrombus.

关 键 词：血管脂肪瘤 临床 病理 

分 类 号：R730.2[医药卫生—肿瘤]