腹部外周性原始神经外胚层肿瘤的临床及CT、MR诊断  

Peripheral primitive neuroectodermal tumors in abdomin:Clinical,CT and MR features

作　　者：莫蕾[1] 江新青[1] 古杰洪[1] 林竹[1] 

机构地区：[1]广州市第一人民医院放射科,广东广州510180

出　　处：《中国医学影像技术》2010年第10期1915-1918,共4页Chinese Journal of Medical Imaging Technology

摘　　要：目的分析腹部外周性原始神经外胚层肿瘤(pPNET)的临床特点、CT与MRI表现。方法对有完整影像学及病理学资料的13例腹部pPNET患者进行回顾性分析。结果本组腹部pPNET的临床特点主要为青少年快速增大的包块伴疼痛,易转移复发,预后差。CT及MRI表现为体积较大、呈浸润性生长的软组织肿块,密度(或信号)不均,常见坏死囊变,无钙化,增强后不均匀强化,可见间隔及网格状强化;病灶对周围正常组织有侵袭,侵犯骨质结构时呈溶骨性骨质破坏,多无骨膜反应及瘤骨。结论腹部pPNET临床表现及CT、MRI表现无明显特征,但CT与MR能较准确描述肿瘤内部结构、毗邻关系及转移情况,对制订治疗方案和评价疗效有重要价值。Objective To analyze the clinical features,CT and MRI findings of abdominal peripheral primitive neuroectodermal tumors （pPNET）. Methods Thirteen patients with pPNETs integrated with data of radiography and pathology were retrospectively analyzed. Results pPNET were commonly seen in youth. The main symptom was fast growing mass with pain. pPNET was poor prognosis with metastases and recurrence. CT and MRI showed a large,heterogeneous,ill-defined soft tissue mass with hypodense cystic areas and non-calcified. Heterogeneous separator and reticular enhancement were seen with the tumors. The tumors tended to invade adjacent tissues,showed lytic bone destruction,whereas no periosteal reaction and neoplastic bone when the bones were involved. Conclusion Clinical and radiological findings of pPENT have not specificity. CT and MR can better demonstrate the internal structure,adjacent tissue relationship and metastases of pPNET,therefore being useful in the planning of the surgical approach and the evaluation of response to treatment.

关 键 词：神经外胚层肿瘤 原始 体层摄影术 X线计算机 磁共振成像 

分 类 号：R730.264[医药卫生—肿瘤] R445.2[医药卫生—临床医学]