血管性血友病患儿行颅缝早闭成型术的围手术期管理：不同寻常的关注目标  

作　　者：Isabelle Maquoi, MD Vincent Bonhomme, MD, PhD Jacques Daniel Born,MD,PhD Marie-Frangoise Dresse, MD, PhD Elisabeth Ronge-Collard,MD Jean-Marc Minon, MD, PhD Pol Hans, MD, PhD 蒋金娣(译) 钱燕宁(校) 

机构地区：[1]University Department of Anesthesia and ICM [2]Department of Neurosurgery [3]University Departmentof Pediatrics [4]Liege Hemophilia Treatment Cente~ [5]Department of Laboratory Medicine,Hemostasis and Thrombosis Unit, CHR Citadelle, Liege, Belgium [6]不详

出　　处：《麻醉与镇痛》2010年第5期69-73,共5页Anesthesia & Analgesia

摘　　要：我们报告一例在手术前评估时诊断为重型I型血管性血友病并用VII因子浓缩剂和瑞斯托霉素辅因子治疗的患儿，成功行颅缝早闭成形术的管理经验。麻醉医师、神经外科医师、临床病理医师和小儿血液科医师的合作是成功的关键。We report the successful management of a craniosynostosis repair in a child with severe Type Ivon Willebrand disease diagnosed during the preoperative assessment and treated by coagulation factor VIII and ristocetin cofactor. Collaboration among the anesthesiologist, the neurosurgeon, the clinical pathologist, and the pediatric hematologist is important for successful management.

关 键 词：血管性血友病 颅缝早闭 围手术期管理 患儿 成型术 神经外科医师 麻醉医师 瑞斯托霉素 

分 类 号：R554.1[医药卫生—血液循环系统疾病]