Dandy-Walker综合征的MRI诊断(附6例报告)  

MRI diagnosis of Dandy-Walker syndorme(report of 6 cases)

作　　者：邹建勋[1] 李旭丹[1] 陈旭高[1] 

机构地区：[1]浙江省丽水市人民医院放射科,浙江丽水323000

出　　处：《医学影像学杂志》2010年第2期156-158,共3页Journal of Medical Imaging

摘　　要：目的:探讨Dandy-Walker综合征(DWS)的临床及MRI表现特征。方法:对6例经MRI诊断为DWS进行回顾性分析。结果:MRI主要表现为小脑蚓部缺如,小脑半球部分发育不全伴分离、移位;第四脑室囊状扩大与后颅窝囊腔相通;后颅窝扩张伴有横窦、窦汇和小脑幕上移;常伴有幕上不同程度梗阻性脑积水及其他颅内畸形。结论:DWS的MRI表现具有特征性,MRI是诊断DWS的最理想的影像学方法。Objective：To explore the clinic and MRI features of Dandy-Walker syndrome（DWS）.Methods：The MRI findings of DWS（n=6） confirmed by MRI scan were analyzed retrospectively.Results：The main MRI findings of DWS were observed as follows： absence of the cerebellar vermis or partial agenesis of the separative cerebellar hemispheres,cystic dialation of the fourth ventricle communicating with enlargement of posterior fossa cyst,enlargement of posterior fossa with upward displacement of lateral sinuses,sinus confluens and tentorium,and often accompanying with differential supratentorial hydrocephalus of obstruction and other intracranial malformations.Conclusion：There are characteristic MRI findings in the DWS and MRI scan is a valuable method for an early diagnosis of DWS.

关 键 词：DANDY-WALKER综合征 后颅窝囊肿 磁共振成像 

分 类 号：R742.82[医药卫生—神经病学与精神病学] R445.2[医药卫生—临床医学]