肾上腺横纹肌肉瘤1例及文献复习  

Epinephros Rhabdomyosarcoma:a Case Report and Review of the Literature

作　　者：阳新华 唐正严[2] 刘宇 田稳[2] 肖仑[2] 

机构地区：[1]湖南省株洲市第一人民医院泌尿外科,湖南株洲412000 [2]中南大学湘雅医院泌尿外科 [3]邵阳市中心医院泌尿外科

出　　处：《临床泌尿外科杂志》2011年第2期111-112,115,共3页Journal of Clinical Urology

摘　　要：目的:探讨肾上腺横纹肌肉瘤(RMS)的临床特征及诊治疗方法。方法:对1例肾上腺横纹肌肉瘤患者的临床资料进行总结,检索Pubmed和CBM数据库相关文献进行复习讨论。结果:患儿通过手术治疗.术后病理检查为右肾上腺区横纹肌肉瘤,免疫组化:Vim(+),Myogenin(+),axtin—横(+),CgA(—),Syn(—),S—100(—),HHF35(—),F8(—),CD34(—),EMA(—)。结论:肾上腺RMS是非常罕见的恶性肿瘤.其肿瘤结构、细胞形态都有一定的特征,确诊需免疫组化染色的帮助,横纹肌肉瘤的治疗和预后在很大程度上取决于手术切除的彻底性和组织类型。Objective： To analyze the clinical features, diagnose and treatment approach of epinephros rhabdomyosarcoma. Methods：A case of epinephros rhabdomyosarcoma was described and the related literature was reviewed in the retrieval of Pubmed and CBM database. Results：The patient was a 5-year old boy,the tumor was removed by operation, The pathology diagnosis was the epinephros rhabdomyosarcoma. Immunohistochemical staining ： Vim（ ＋ ）, Myogenin（ ＋ ）, axtin-rhabdomyosarcoma （ ＋ ）, CgA （ - ）, Syn （ - ）, S-100 （ - ）, H HF35 （ - ）, F8 （-）,CD34（-）, EMA（-）. Conclusions： Epinephros rhahdomyosarcoma is extremely rare. It should be identified from other tumors by the Immunohistochemieal staining. And the cure and prognosis of the rhabdomyosareoma depends on thorough exairesis and tissue type.

关 键 词：肾上腺 横纹肌肉瘤 病理诊断 免疫组织化学 

分 类 号：R736.6[医药卫生—肿瘤]