表现为脑干受损的颈内动脉海绵窦瘘的临床特点(附3例报告)  

Clinical features of carotid-cavernous fistula which manifested as brainstem damage(report of 3 cases)

作　　者：钱敏[1] 石静萍[1] 蒋惟伟[2] 刘文[2] 肖朝勇[2] 

机构地区：[1]南京医科大学附属脑科医院神经内科,210029 [2]南京医科大学附属脑科医院放射科,210029

出　　处：《临床神经病学杂志》2010年第6期425-427,共3页Journal of Clinical Neurology

摘　　要：目的探讨表现为脑干受损的颈内动脉海绵窦瘘(CCF)的临床特点。方法回顾性分析3例表现为脑干受损的CCF患者的临床资料。结果本组患者主要表现为脑干功能障碍,伴轻度脑神经受损症状,未见眼球突出及球结膜充血的眼部症状。颅脑MR I显示中脑、脑桥、延髓较大长T1、长T2异常信号,丘脑底节区可见小片状长T1、长T2异常信号,增强扫描部分病灶强化;3例MRA均提示CCF;2例DSA确诊为CCF。结论表现为脑干受损的CCF患者临床上缺乏典型的眼球突出、球结膜充血及颅内血管杂音三联征,但MR I可显示其脑干病灶。Objective To investigate the clinical features of carotid-cavernous fistula（CCF） which manifested as brainstem damage.Methods The clinical data of 3 CCF patients who manifested as brainstem damage were analyzed retrospectively.Results The main clinical features of this group were symptoms relating to brainstem dysfunction and mild cranial nerves damage,but without eye symptoms like exophthalmos and conjunctiva hyperemia.Brain MRI showed that large abnormal signals of T1 and T2 in midbrain,pons and medulla.There were small pieces abnormal signals of T1 and T2 in thalamus.Some foci were enhanced by enhancement scanning.The diagnosis of CCF in the 3 cases was indicated by MRA.The definitely diagnosis of CCF in 2 cases were made by DSA.Conclusions The typical three union syndrome including exophthalmos,conjunctiva hyperemia and cranial vascular souffle is deficiency in CCF patient who manifested as brainstem damage.MRI can show the foci in brainstem.

关 键 词：颈内动脉海绵窦瘘 脑干 

分 类 号：R743[医药卫生—神经病学与精神病学]