长骨造釉细胞瘤的影像诊断(附1例报道并文献复习)  

Case report and literature review of adamantinoma of long bone

作　　者：高振华[1] 陈应明[1] 关键[1] 孟悛非[1] 

机构地区：[1]中山大学附属第一医院医学影像科,广州510080

出　　处：《影像诊断与介入放射学》2010年第6期341-343,共3页Diagnostic Imaging & Interventional Radiology

摘　　要：目的结合文献探讨长骨造釉细胞瘤的临床、影像和病理学特点,以提高术前诊断水平。方法回顾性分析1例胫骨造釉细胞瘤影像学资料并复习国内外有关长骨造釉细胞瘤文献。结果国内文献复习显示长骨造釉细胞瘤多见于20岁以上青壮年(约占86.3%),好发于胫骨干(约占90%);涉及X线描述的39例文献报道中,34例(占87.2%)表现为边界清楚的单囊或多囊状骨质破坏,其中61.8%例有膨胀性改变,26.5%例出现骨皮质部分缺失,38.2%例伴有明显的骨质增生硬化,均未见骨膜新生骨。病理学呈上皮性和纤维性双向分化表现。本例患者基本符合上述特点。结论长骨造釉细胞瘤罕见,若20岁以上患者胫骨干出现良性骨肿瘤一般影像学特征或兼有部分恶性骨肿瘤表现时应考虑本病的可能。Objective To analyze the clinical, imaging and pathological features of adamantinoma of long bone to aid preoperative diagnosis. Methods A case of adamantinoma of long bone was reported and the related literature was reviewed. Results Literature review showed that long bone ameloblastoma was more common in young adults older than 20 years of age （86.3%） and occurred mainly in the tibial shaft （90%）. The clinical, imaging and pathological features in our patient were consistent with those reported in the literature. Among 39 cases in the Chinese litera- tun, radiographic findings included uni- or multi-cystic bone destruction with well-defined borders （87.2%）, bone expansion （61.8%）, partial loss of cortical bone （26.5%）, bone sclerosis （38.2%）, and no periosteal new bone reaction （100%）. Pathology showed epithelial and fibrous differentia- tion. Conclusion Adamantinoma of long bone should be considered in patients older than 20 years of age with tibial lesions that have imaging characteristics of benign bone tumors or some malignant features.

关 键 词：造釉细胞瘤 长骨 磁共振成像 

分 类 号：R738.1[医药卫生—肿瘤]