成人腹膜后节细胞神经纤维瘤1例暨文献复习  

Case Report:One case of adult's retroperitoneal ganglioneuroma

作　　者：唐俊伟[1,2] 章素芬[1,2] 金宇飚[1] 戴雪明[1] 王海权[1] 刘俊[1] 

机构地区：[1]上海市第一人民医院普外科,上海200080 [2]南京医科大学,江苏南京210029

出　　处：《现代生物医学进展》2011年第6期1132-1134,共3页Progress in Modern Biomedicine

摘　　要：原发性腹膜后节细胞神经纤维瘤在临床上是属于极少见的病例,通常患者就诊时无明显临床症状。本文报道1例43岁成年男性的腹膜后节细胞神经纤维瘤并进行相关文献的复习。已有研究证实影像学检查可对原发性腹膜后肿瘤的良恶性鉴别提供重要依据,节细胞神经纤维瘤的影像学检查亦具有其特征性表现,但最终本病的确诊仍依赖病理及免疫组化技术。影像学检查是确定原发性腹膜后肿瘤的治疗计划的必要措施。目前手术已成为治疗腹膜后节细胞神经纤维瘤的首选治疗。辅以血管外科技术,肿瘤的根治性切除已在临床上广泛开展。通过手术治疗后尽管有二次复发可能,但腹膜后节细胞神经瘤预后仍较好。The primary retroperitoneal ganglioneuroma（PRG） is a very infrequent disease.The case of a 43-year-old male who presented with a 9.2cm primary retroperitoneal ganglioneuroma is presented,and the relevant literature is reviewed.Research has com-firmed that imaging examination plays an important role in differentiating whether the primary retroperitoneal tumor is malignant or not,while the PRG has the characteristics of imaging examination itself.Pathology and the immunohistochemisty test is the Golden standard of the disease.The selection of the treatment plan depends on the results of the pathology and immunohistochemisty test.Recently,oper-ation has become the primary treatment of PRG.Assisting by the technique of cardiovascular surgery,radical excision has been widely carried out.In spite of the recurrence,the PRG shows a good prognosis in general.

关 键 词：腹膜后肿瘤 节细胞神经纤维瘤 病例报告 

分 类 号：R730[医药卫生—肿瘤] R735.4[医药卫生—临床医学]