成人烟雾病的临床和影像学特点(附26例报告)  

CLINICAL AND IMAGING CHARACTERISTICS OF MOYAMOYA DISEASE IN ADULTS:A REPORT OF 26 CASES

作　　者：刘丽君[1] 张晨[1] 

机构地区：[1]青岛大学医学院附属医院神经内科,山东青岛266003

出　　处：《青岛大学医学院学报》2011年第3期242-244,共3页Acta Academiae Medicinae Qingdao Universitatis

摘　　要：目的分析成人烟雾病的临床和影像学特点。方法对26例经DSA确诊的成人烟雾病病人的临床和影像学资料进行回顾性分析。结果本组缺血性卒中占69.2%,临床表现以偏瘫、肢体麻木、失语常见;出血性卒中占30.8%,临床表现以头痛、意识障碍、偏瘫常见。所有病人均有颈内动脉或其分支狭窄或闭塞和烟雾血管形成。结论成人烟雾病临床表现多样,但以脑缺血最常见。临床上遇到青年卒中;无脑卒中危险因素的病人出现脑梗死,尤其是脑叶梗死;反复多次发生短暂性脑缺血发作(TIA)或脑梗死;两侧交替的TIA或脑梗死;无卒中危险因素的病人出现脑室或脑室周围出血、脑叶出血;颅脑CT或MRI显示多发性脑梗死或出血、出血并梗死者应高度警惕烟雾病的可能。Objective To analyze the clinical and imaging features in adult moyamoya patients.Methods Clinical and imaging data of 26 adult patients with moyamoya confirmed by DSA were analyzed retrospectively.Results Of the 26 patients,ischemic stroke accounted for 69.2%,with hemiplegia,hemianesthesia and aphasia being commonly seen;Hemorrhagic stroke accounted for 30.8%,common manifestations included headache,disturbance of consciousness and hemiplegia.Stenosis or occlusion of the internal carotid artery or its branches and moyamoya vessels were found in all the patients.Conclusion The manifestations of adult moyamoya patients were diverse,in which,cerebral ischemia was the most commonly seen.The possibility of moyamoya disease should be on high alert when the following conditions were met： apoplexy in the youth;cerebral infarction,especially in lobe of brain,occurred in patients with no risk factors of the disease;those with repeated TIA or cerebral infarction;alternating TIA or cerebral infarction of two sides;periventricular or ventricular or hemorrhage of lobe of brain;multiple cerebral infarction or hemorrhage,hemorrhage accompanied by infarction revealed on CT or MRI.

关 键 词：脑底异常血管网病 临床特征 影像学特点 诊断 

分 类 号：R743.3[医药卫生—神经病学与精神病学]