肝脏上皮样血管平滑肌脂肪瘤1例临床病理特征分析及文献复习  

Hepatic epithelioid angiomyolipoma: A case report and literature review

作　　者：张斌[1] 吕自力[2] 覃晓[3] 彭民浩[3] 彭涛[3] 

机构地区：[1]广西医科大学研究生学院 [2]广西医科大学第一附属医院病理科 [3]广西医科大学第一附属医院肝胆血管外科,南宁530021

出　　处：《中国癌症防治杂志》2011年第2期120-125,共6页CHINESE JOURNAL OF ONCOLOGY PREVENTION AND TREATMENT

基　　金：国家自然科学基金(NSFC81072321;NSFC30960021-C010803);广西医疗卫生重点科研课题基金(重201018)资助课题

摘　　要：目的回顾分析1例肝脏上皮样血管平滑肌脂肪瘤(epithelioid angiomyolipoma,EAML)的临床和病理学特点,结合文献复习为临床诊断及治疗提供参考。方法详尽分析1例肝脏EAML的临床、影像学及病理学特点,结合文献复习进行讨论。结果对肝左内叶单发巨大占位行左半肝切除术,术中及术后均未使用抗肿瘤药物治疗,随访15个月无瘤生存。结论肝脏EAML临床极为罕见,术前诊断困难且有恶性潜能,目前治疗仍首选肿瘤切除术,对抗肿瘤药物治疗尚无统一认识,术后密切随访对进一步明确其肿瘤生物学行为特征极为重要。Objective To analyze retrospectively the clinical and pathological features of a case of hepatic epithelioid angiomyolipoma,with literatures review.Methods The clinical,radiological and pathological features of the case were analyzed,and the related literatures were reviewed.Results The case received left lobe hepatectomy and has been 15-months of tumor-free survival.Conclusions Hepatic epithelioid angiomyolipoma is extremely rare and difficult to diagnose before operation.Due to its malignant potential,surgical resection is recommended and close follow-up is important to confirm its biology feature.There is no agreement on chemotherapy regime for this neoplasm.

关 键 词：肝脏 肿瘤 上皮样血管平滑肌脂肪瘤 

分 类 号：R735.7[医药卫生—肿瘤]