41例成人烟雾病的临床特点及血管影像学分析  

Clinical and imaging characteristics of Moyamoya disease: report of forty-one cases

作　　者：张萍[1] 梅翠红[1] 陈黛琪[1] 田代实[1] 李倩[1] 骆翔[1] 

机构地区：[1]武汉华中科技大学同济医学院附属同济医院神经内科,湖北430030

出　　处：《脑与神经疾病杂志》2011年第6期403-407,共5页Journal of Brain and Nervous Diseases

基　　金：国家青年自然科学基金(81000521)

摘　　要：目的总结成人烟雾病的临床及血管影像学特点。方法回顾性分析41例成人烟雾病的临床表现及影像学资料,以观察其临床及影像学特点。结果本组患者多为青壮年起病,平均起病年龄40岁左右,无明显性别差异;均以脑卒中形式急性起病,缺血性卒中占19.5%,出血性卒中占80.5%;DSA表现为Willis环附近动脉狭窄或闭塞,脑底烟雾状血管网、侧枝循环及动脉瘤形成。结论青壮年反复发作的脑卒中,尤其是无高血压病及动脉硬化证据时,应警惕烟雾病的可能,需行全脑DSA检查以明确诊断。Objective To analyze the clinical and digital subtraction angiography （DSA） features of adult patients with Moyamoya disease. Methods 41 patients who were diagnosed as Moyamoya disease were investigated. The clinical representation and DSA imagines were observed. Results This disease primarily ＇affected youth and middle-ages, with an average age of 40 years. No conspicuous difference between male and temale. The forms of disease onset were all acute cerebral accidents. 19.5% was ischemic type, while 80.5% was hemorrhage t）pe. DSA couhl find vascular stenosis or occlusion in the circle of willis and collateral circulation formed to compensate. Aneurysm formed in some cases. Conclusion Moyamoya disease should be considered when stroke recurrently attacks in youth and middle-ages, especially without risk factors. DSA should be performed in order to identify diagnosis.

关 键 词：烟雾病 数字减影脑血管造影 

分 类 号：R742.5[医药卫生—神经病学与精神病学]