儿童门静脉海绵样变性的研究进展  

Current research of cavernous transformation of portal vein for children

作　　者：张丹 陈亚军 张廷冲 

机构地区：[1]北京新世纪儿童医院外科,北京100045

出　　处：《国际外科学杂志》2012年第2期118-121,共4页International Journal of Surgery

摘　　要：门静脉海绵样变性约占小儿门静脉高压的40％。与其他引起门静脉高压的病种相比，该病有发病年龄早、出血危险性高及肝功能大致正常等特点。由于病因相对单一，大多数患儿无合并其他疾病，因此合理的治疗对该病的预后有决定性意义。目前对于该病的诊疗理念国内外存在较大差异，国内仍将治疗目的主要集中在控制消化道出血方面，而国外对于该病的治疗则放在术后患儿肝脏血流灌注的改善、脾功能亢进的缓解、术后生活质量等方面，本文旨在总结近几年国外相关文献，介绍目前国外对于该病的最新研究成果。Cavernous transformation of portal vein accounts for about 40% in children portal hypertension. Compared with other causes of portal hypertension disease cavernous transformation of portal vein presents early age of disease onset, high risk of bleeding and normal liver function. Because the pathology is relatively simple and most children have no other diseases, so a reasonable treatment of the disease has deci- sive significance. The current concept for diagnosis and treatment of the disease is different between home and abroad, Controlling upper gastrointestinal bleeding is the main purpose in out country. Reliving hypersplenism, improving liver blood supply and quality of life are much important abroad, The article aims to summarize latest foreign literature to introduce latest research for the disease abroad.

关 键 词：门静脉海绵样变性 Rex术式 肝脏血供 门腔静脉分流术 

分 类 号：R575.2[医药卫生—消化系统]