原发性肺动脉肉瘤临床病理观察  

Primary pulmonary artery sarcoma:clinical and pathological analyses

作　　者：汪静皎[1] 杨国仪[1] 张丽华[1] 杨树东[1] 

机构地区：[1]南京医科大学附属无锡市人民医院病理科,江苏无锡214023

出　　处：《诊断病理学杂志》2012年第2期129-131,共3页Chinese Journal of Diagnostic Pathology

摘　　要：目的探讨原发性肺动脉肉瘤(PAS)的临床病理学特征。方法结合相关文献,对1例原发性肺动脉肉瘤的临床病理学特征进行分析。结果原发性肺动脉肉瘤多为内膜肉瘤,镜下多表现为多形性肉瘤的图像,免疫表型缺乏特异性,临床表现与肺血栓栓塞症相似。结论 PAS是一种非常罕见的肿瘤,多表现为纤维母细胞及肌纤维母细胞分化,预后很差。Objective To study the clinical-pathological features and significant prognostic factors of primary pulmonary artery sarcoma（PAS）.Methods Clinical data of one patient with pulmonary artery sarcoma in Wuxi Peoples Hospital were retrospectively analyzed and related literature were reviewed.Results Pulmonary artery sarcoma had similar clinical presentations to pulmonary thromboembolism.Most of the PAS were intimal sarcoma which had the pattern of pantomorphia sarcoma.The immunophenotype of PAS default specificity.Conclusions Pulmonary artery sarcoma is a very rare poorly differentiated mesenchymal tumor with fibroblastic and myofibroblast differentiation which has a poor prognosis.

关 键 词：原发性 肺动脉 内膜肉瘤 病理学特征 

分 类 号：R732.21[医药卫生—肿瘤]