原发性脑室出血型Moyamoya病21例临床分析  

Clinical features of the primary intraventricular haemorrhagic type moyamoya disease

作　　者：陈骅[1] 罗良生[1] 张健[1] 林忠[1] 王东[1] 廖萍[1] 吴有志[1] 吴鸣[1] 

机构地区：[1]南京医科大学附属南京第一医院神经外科,南京210029

出　　处：《立体定向和功能性神经外科杂志》2011年第5期290-293,共4页Chinese Journal of Stereotactic and Functional Neurosurgery

摘　　要：目的通过回顾性分析我院10年来收治的21例原发性脑室出血型Moyamoya病患者的临床资料,探讨非高血压性原发性脑室出血与Moyamoya病及其影像学特征的关系。方法对我院神经外科10年来确诊的原发性脑室出血Moyamoya病患者的CT、DSA和临床治疗进行回顾性分析。结果 25例非高血压性原发性脑室出血患者中DSA证实21例为Moyamoya病。3例合并基底动脉动脉瘤。所有患者出血侧均存在脉络膜前动脉异常扩张扭曲及异常分支。该组患者首次治疗均获得良好结果。结论 Moyamoya病是成人非高血压性原发性脑室出血的主要病因,对成人非高血压性原发性脑室出血应常规行DSA明确是否存在Moyamoya病。成人非高血压性原发性脑室出血与脉络膜前动脉的扩张扭曲或异常分支密切相关,并且后者可作为前者的预测指标。Objective To investigate the relationship among non-hypertensive primary intraventricular hemorrhage,moyamoya disease and angiographic changes,we reviewed the clinical data of 21 adult patients with primary intraventricular haemorrhagic type moyamoya disease.Methods CT,DSA and clinical data of primary intraventricular haemorrhagic type moyamoya disease were reviewed.Results 21 patients in 25 non-hypertensive primary intraventricular hemorrhage were diagnosed as Moyamoya Disease.Moyamoya disease associated with basilar artery aneurysm was comfirmed in three patients.Angiographic dilatation and branch extension of the anterior choroidal artery were found in each haemorrhagic hemisphere.All patients received initial treatment obtained good results.Conclusion Moyamoya disease is the major cause of adult non-hypertensive primary intraventricular hemorrhage.Non-hypertensive adults with primary intraventricular hemorrhage should be conventionally inspected for moyamoya disease by DSA.Adult non-hypertensive primary intraventricular hemorrhage and angiographic dilatation and branch extension of the anterior choroidal artery is closely related.And the latter can be used as a predictor of the former.

关 键 词：原发性脑室出血 MOYAMOYA病 脉络膜前动脉 

分 类 号：R743.34[医药卫生—神经病学与精神病学]