肝豆状核变性并肝硬化的MR诊断  

MR Manifestations of Cirrhosis in Hepatolenticular Degeneration

作　　者：杨清华[1] 王穗春[1] 刘爱群[1] 王波[1] 

机构地区：[1]广东药学院附属第一医院,广东广州510080

出　　处：《中国医学创新》2012年第16期91-92,共2页Medical Innovation of China

摘　　要：目的:探讨肝豆状核变性并肝硬化的MR表现,以期早期诊断。方法:对20例明确诊断为肝豆状核变性伴肝硬化患者的MR的表现进行回顾性分析。结果:肝、脾增大者8例;3例表现为肝脏多发再生结节,体积萎缩,肝裂增宽;6例表现为再生结节形成,肝脏体积萎缩,肝裂增宽,同时门静脉增宽,脾脏增大;3例表现为再生结节形成,门静脉增宽、脾大同时合并食道下段及胃冠状静脉曲张。结论:肝豆状核变性伴肝硬化MR检出率为100%,其MR表现具有一定的特征性,是早期诊断无神经系统锥体外系症状的肝豆状核变性的重要证据。Objective:To explore the MR manifestations of cirrhosis in hepatolenticular degeneration to early diagnosis of it.Methods:Retrospective analysis of the MR fnddings of 20 Indeed dagnosed cirrhosis in hepatolenticular degeneration.Results:8 cases of patients showed liver and spleen enlargement;3 cases showed multiple regenerative nodules in the liver,shrinking liver volume,liver crack widened;6 cases of patients showed multiple regenerative nodules in liver volume atrophy,liver crack widened,and the portal vein was widened,the spleen enlargement;3 cases of patients showed multiple regenerative nodules,portal hypertension with lower esophageal and gastric coronary varices.Conclusion:There is a certain characteristic of MR appearance of cirrhosis in hepatolenticular degeneration and it is the early diagnosis of extrapytamidal symptoms in the nervous system,liver degeneration of important evidence.

关 键 词：肝豆状核变性 肝纤维化 肝硬化 磁共振成像 

分 类 号：R575.2[医药卫生—消化系统]