肝脏Kasabach—Merritt综合征的诊疗进展  

Progress in the diagnosis and treatment of hepatic Kasabach- Merritt syndrome

作　　者：林汉[1] 麻勇[1] 刘连新[1] 

机构地区：[1]哈尔滨医科大学附属第一医院肝脏外科；教育部肝脾外科重点实验室,150001

出　　处：《中华肝胆外科杂志》2012年第6期486-488,共3页Chinese Journal of Hepatobiliary Surgery

基　　金：黑龙江省高校科技创新团队建设计划资助（2009td06）

摘　　要：肝脏Kasabach—Merritt综合征是一种高潜在致死性复杂肝脏血管癯的严重并发症。该综合征临床罕见，容易造成误诊、误治，甚至危及生命。目前该病缺乏系统性研究报道。为提高对该病的认识，本文就肝脏Kasabach-Merritt综合征的发病机制、诊断、综合治疗、预后和转归情况作一综述。Hepatic Kasabach-Merritt syndrome （KMS） is a highly complex and potentially fatal complication of severe hepatic hemangioma. Although hepatic KMS is rare, the death rate of victims is significant because it is of- ten misdiagnosed upon presentation and thus receives im- proper treatment. Presently the literature lacks a systematic review of hepatic KMS. We have summarized its pathogene- sis, diagnosis, systematic treatment, prognosis and out- comes in order to increase awareness of this deadly disease.

关 键 词：肝脏Kasabach—Merritt综合征 血管瘤 血小板减少症 

分 类 号：R735.7[医药卫生—肿瘤]