儿童外周型原始神经外胚层肿瘤的CT、MRI表现  

Imaging Findings of Pediatric Peripheral Primitive Neuroectodermal Tumor

作　　者：唐雯娟[1] 吴伟军[1] 张军[1] 韩燕乔[1] 

机构地区：[1]上海交通大学附属儿童医院放射科,200042

出　　处：《临床放射学杂志》2012年第10期1454-1457,共4页Journal of Clinical Radiology

摘　　要：目的探讨儿童外周型原始神经外胚层肿瘤(peripheral primitive neuroectodermal tumor,pPNET)的CT、MRI表现,提高对该病的诊断水平。方法回顾性分析14例经手术病理证实的儿童pPNET的临床、CT、MRI及病理组织学表现,并复习相关文献。结果 14例患儿中,肿瘤分别位于颈部(3例),胸部(4例),脊柱旁(3例),盆腔(2例)及四肢(2例);3例肿瘤均呈不均质囊实性密度或信号,11例为实性密度或信号。CT平扫密度低于肌肉组织,未见明显钙化,周围骨性组织多可见硬化或虫蚀样破坏,部分可见骨膜反应。MR T1WI肿块呈等低信号,T2WI、短恢复时间反转恢复法(STIR)呈不均质混杂高信号,增强扫描明显不均匀强化,中心囊变、坏死区未见明显强化。结论儿童pPNET缺乏典型的特异性影像学表现,但具有一定的影像学特点。CT和MRI有助于鉴别诊断、制定手术计划。Objective To analyze CT and MRI findings of pediatric peripheral primitive neuroectodemal tumor（pPNET） for improving the level of diagnosis.Methods To report clinic,CT,MRI findings and pathologic results of 14 pediatric pPNET.Results Among 14 tumor in 14 children,3 were located in cervical part,4 in thoracic part,3 aside spine,2 in pelvic cavity.As for density and signal,3 were heterogeneous or ascoma,11 were parenchymatous.CT attenuations were lower than muscles and without calcification.There were osseous scleroses or eroded edges in most of the tumors.Periosteal proliferation was found in some cases.The tumor signals were equal or low on T1WI,and heterogeneous or high on T2WI and STIR.After injection of contrast agents,parenchyma enhanced heterogeneous while cystic and necrotic tissue did not.Conclusion There are no typical imaging findings on pediatric pPNET.However,it has some imaging characteristics.CT and MRI are helpful in differential diagnosis and making operation protocol.

关 键 词：儿童 外周型原始神经外胚层肿瘤 体层摄影术 X线计算机 磁共振成像 

分 类 号：R739.4[医药卫生—肿瘤]