原发性肝淀粉样变性1例  

Primary hepatic amyloidosis:A case report

作　　者：刘亚萍[1] 刘欣[1] 张宽学[1] 赵江涛[1] 黄苗[1] 

机构地区：[1]西安交通大学医学院第二附属医院消化内科,陕西省西安市710004

出　　处：《世界华人消化杂志》2012年第31期3065-3067,共3页World Chinese Journal of Digestology

摘　　要：患者,男,52岁,因上腹饱胀不适半年,伴乏力、头晕3mo入院,近1年来测血压低,查体发现肝脏肿大,碱性磷酸酶升高伴转氨酶轻度升高,有少量腹水及心包积液,肝穿刺活检经光镜及电镜检查均考虑肝淀粉样变性,该病在临床上较为罕见,诊断靠病理检查,尚无特异治疗方法,预后较差.A 52-year-old male patient was admitted because of distention and discomfort in the upper abdomen for six months,fatigue and anorexia for three months,and low blood pressure for one year.Physical examination revealed enlargement of the liver.He had an elevated alkaline phosphatase（ALP） level and a slightly increased transaminase level.A small amount of ascites and pericardial effusion were noted.Both light microscopy and electron microscopy following liver biopsy suggest hepatic amyloidosis.Hepatic amyloidosis is an extremely rare clinical entity that portends a poor prognosis.The diagnosis depends on pathological examination,and there is no special therapy.

关 键 词：肝脏疾病 淀粉样变性 原发性 

分 类 号：R575.5[医药卫生—消化系统]