以下肢病变为主的Klippel-Trenaunay综合征的诊治新进展  

Advances in Diagnosis and Treatment of Klippel-Trenaunay Syndrome with Lower Extremity Lesions as Main Symptom

作　　者：那金波[1] 刘冰[1] 唐波[1] 

机构地区：[1]哈尔滨医科大学附属第一医院血管外科,哈尔滨150001

出　　处：《医学综述》2012年第23期4012-4015,共4页Medical Recapitulate

摘　　要：Klippel-Trenaunay综合征(KTS)是一种先天性周围血管疾病。一般以下肢单纯浅静脉异常畸形较为常见,临床上以葡萄酒色斑痣、异位浅静脉曲张伴深静脉正常或阙如以及肢体肥大三联征最为常见。病因尚不明确,发病机制与先天性坐骨静脉系未闭合有关。目前,KTS的诊断主要依靠数字减影血管造影或者CT,明确诊断后行合理的手术治疗可极大地改善患者的生活质量。Klippel-Trenaunay syndrome（KTS）is a congenital peripheral vascular disease.Simple and shallow lower limb venous anomaly deformity is more commonly seen.Wine stain pole,ectopic varicose veins associated with deep vein normal or lacking,and limb hypertrophy triad is the most common in clinic.The etiology is unclear,the pathogenesis is related with unclosed congenital ischial venous system.The diagnosis of KTS relies on DSA or CT.Implementation of reasonable surgical treatment after diagnosis can greatly improve patients′ quality of life.

关 键 词：KLIPPEL-TRENAUNAY综合征 影像检查 手术治疗 介入治疗 

分 类 号：R739[医药卫生—肿瘤]