21羟化酶缺乏致女性假两性畸形的内外科联合治疗  

Combined treatment of pseudohermaphroditism

作　　者：李伯达[1] 夏兆骥[2] 陈德波[1] 林泽旭[1] 袁志明[1] 

机构地区：[1]泉州市第一医院整形外科,泉州362000 [2]北京医科大学第三医院成形科

出　　处：《中华整形外科杂志》2000年第4期206-207,共2页Chinese Journal of Plastic Surgery

摘　　要：目的　为了诊断和治疗 2 1羟化酶缺乏导致的女性假两性畸形。方法　 1990年以来 ,对 4例患者进行了外科手术和内科糖皮质激素的综合治疗。结果　 4例均得到了一个较完善的女性外阴 ,补充治疗了由于 2 1羟化酶先天缺乏引起的一系列全身症状。结论　综合治疗使该病在临床上获得了满意结果。Objective\ To diagnose and treat female pseudohermaphroditism caused by 21\|hydroxylase deficiencies.Methods\ Four female patients with 21\|hydroxylase deficiencies have received combined treatment of reconstructive surgery and supplementary glucocorticoid in our hospital since 1990.Results\ The patients obtained a female external genitalias through teh operation.Various symptoms resulted from 21\|hydroxylase deficiency were improved with glucocorticoid therapy.Conclusion\ A satisfying result can be achieved for pseudohermaphroditism by combination of surgery and medicine.\;

关 键 词：21羟化酶缺乏 假两性畸形 外科手术 糖皮质激素 

分 类 号：R711.7[医药卫生—妇产科学]