结节性硬化症伴发肝肾血管平滑肌脂肪瘤的CT表现  

CT Findings of Tuberous Sclerosis Associated with Hepatic and Renal Angiomyolipomas

作　　者：李跃兴[1] 向军益[1] 李洁[1] 丁建平[1] 林上奇[2] 

机构地区：[1]杭州师范大学附属医院放射科,杭州310015 [2]杭州市红十字会医院放射科,杭州310015

出　　处：《中国医学科学院学报》2013年第2期136-139,共4页Acta Academiae Medicinae Sinicae

摘　　要：目的描述结节性硬化症伴发的肝、肾血管平滑肌脂肪瘤的CT表现,并分析二者的相关性。方法回顾性分析7例经临床及影像学检查确诊的结节性硬化症的CT表现。结果颅脑CT显示侧脑室室管膜下钙化结节和/或非钙化结节6例;腹部CT显示双肾血管平滑肌脂肪瘤7例,其中2例同时伴发肝血管平滑肌脂肪瘤;胸部CT显示淋巴管肌瘤病1例。结论结节性硬化症的肝、肾血管平滑肌脂肪瘤具有典型的影像学特征,并且肝血管平滑肌脂肪瘤与双肾血管平滑肌脂肪瘤具有相关性,影像学检查具有重要的价值和临床意义。ous sclerosis （TS） the clinical and CT Objective To summarize the clinical and computed tomographic （CT） findings of tuber- associated with hepatic and renal angiomyolipomas. Method We retrospectively analyzed findings of 7 TS patients with hepatic and renal angiomyolipomas. Results Brain CT showed calcified nodules and/or the uncalcified nodule in the lateral ventricle subependymal in 7 patients. Abdominal CT showed bilateral renal angiomyolipomas in 7 cases and hepatic angiomyolipomas in 2 cases. Chest CT showed lym- phangioleiomyomatosis in one case. Conclusions TS associated with merger hepatic and/or renal angiomyoli- pomas have typical CT findings. Liver angiomyolipomas shows certain correlation with bilateral renal angiomyo- lipomas.

关 键 词：结节性硬化症 血管平滑肌脂肪瘤 CT 

分 类 号：R814.42[医药卫生—影像医学与核医学]