母细胞性浆细胞样树状突细胞肿瘤  

Bastic plasmacytoid dendritic cell neoplasm:a case report

作　　者：张敏[1] 颜文良[1] 胡文星[1] 邓德权[1] 谢其美[1] 桑红[1] 

机构地区：[1]南京军区南京总医院皮肤科,江苏南京210002

出　　处：《临床皮肤科杂志》2013年第9期536-538,共3页Journal of Clinical Dermatology

摘　　要：报告1例母细胞性浆细胞样树状突细胞肿瘤。患者男,62岁。以皮肤最先受累,后很快累及全身系统。皮损组织病理学特点为真皮内肿瘤细胞弥漫性浸润,免疫组化显示CD43(+++)、CD4(++)、CD123(++)、CD56(++)。诊断:母细胞性浆细胞样树状突细胞肿瘤。A case of blastic plasmacytoid dendritic cell neoplasm （BPDCN） is reported. Patient＇s clinical manifestations, lab- oratory tests, pathological characteristics, and treatment are also discussed along with literature review. A 62-year-old man presented first with asymptomatic multiple skin lesions and later with involvement of multisystem. Histopathologically, the tumor cells diffusely infiltrated the dermis. Immunohistochemical staining showed that the tumor cells were positive for CD43, CD4, CD123 and CD56. The diagnosis was BPDCN.

关 键 词：母细胞性浆细胞样树状突细胞肿瘤 

分 类 号：R730.263[医药卫生—肿瘤]