获得性凝血因子ⅩⅢ缺乏致严重出血1例  

A case of severe bleeding due to acquired factor ⅩⅢ deficiency

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作  者:胡慧仙[1] 贾永清[1] 金莱[1] 

机构地区:[1]金华市中心医院血液科,浙江金华321000

出  处:《临床血液学杂志》2013年第5期655-656,共2页Journal of Clinical Hematology

摘  要:凝血因子XⅢ(coagulationfactorXⅢ,FXⅢ)又称为纤维蛋白稳定因子,是构成稳定的纤维蛋白凝块所必需的凝血因子,其缺乏可能会导致临床上严重的出血表现。Summary Coagulation factor X m (FX UI ) is a necessary coagulation factor to form a stable fibrin clot,lack of which may result in severe bleeding. Activated FX Ⅲ has an effect of hemostasis. Hereditary FX HI deficiency is a rare autosomal recessive genetic disease,and acquired FX Ⅲ deficiency induced by FX Ⅲ inhibitor is an extreme- ly rare disease. Then we will report a case of severe bleeding due to acquired FX Ⅲ deficiency.

关 键 词:凝血因子ⅩⅢ 出血 抑制物 

分 类 号:R733.7[医药卫生—肿瘤]

 

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