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出 处:《临床血液学杂志》2013年第5期655-656,共2页Journal of Clinical Hematology
摘 要:凝血因子XⅢ(coagulationfactorXⅢ,FXⅢ)又称为纤维蛋白稳定因子,是构成稳定的纤维蛋白凝块所必需的凝血因子,其缺乏可能会导致临床上严重的出血表现。Summary Coagulation factor X m (FX UI ) is a necessary coagulation factor to form a stable fibrin clot,lack of which may result in severe bleeding. Activated FX Ⅲ has an effect of hemostasis. Hereditary FX HI deficiency is a rare autosomal recessive genetic disease,and acquired FX Ⅲ deficiency induced by FX Ⅲ inhibitor is an extreme- ly rare disease. Then we will report a case of severe bleeding due to acquired FX Ⅲ deficiency.
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