儿童肝脏间叶性错构瘤的CT表现与临床病理研究  

CT manifestations and clinical pathology features of hepatic mesenchymal hamartoma in children

作　　者：孙雪峰[1] 袁新宇[1] 杨梅[1] 张晓伦[2] 邹继珍[3] 郭红伟[1] 刘霞[1] 

机构地区：[1]首都儿科研究所附属儿童医院放射科,100020 [2]首都儿科研究所附属儿童医院外科,100020 [3]首都儿科研究所附属儿童医院病理科,100020

出　　处：《中华放射学杂志》2013年第10期917-920,共4页Chinese Journal of Radiology

摘　　要：目的 探讨儿童肝脏间叶性错构瘤（HMH）的CT影像特点,提高术前诊断正确率.方法 搜集经病理证实的HMH9例,其中男4例,女5例,年龄为3d至9岁5个月（中位年龄为7个月）.术前均进行CT平扫及增强扫描.结果 本组9例均为单发肿瘤,位于右叶6例,位于左叶2例,累及两个肝叶1例.瘤体长径约7.0～22.5 cm,平均约13.5 cm.CT表现取决于肿瘤囊实性成分比例和分布,表现为1例为囊性型肿瘤,5例为实性为主的囊实混合型肿瘤,3例为实性型肿瘤,增强后肿瘤实性部分及分隔强化,囊性部分无强化,1例病灶见点状钙化,所有病例均可见肿瘤推压相邻血管,使之变形、移位.结论 儿童HMH的CT表现多样,但有一定特征性,可反映大体病理变化,了解其CT影像特点,结合临床特征,有助于早期诊断.Objective To investigate the CT features of hepatic mesenchymal hamartoma （HMH）in children.Methods Nine patients with HMH confirmed by postoperative pathology were enrolled,including 4 were males and 5 were females.Their age ranged from 3 days to 9 years 5 months （the median age was 7 months）.All patients admitted due to palpable abdominal mass without jaundice.All patients were examed by contrast-enhanced CT before the operation.Results All the 9 cases showed solitary hepatic mass,among which 6 were in the right lobe,2 were in the left lobe and 1 involved in both lobes.The tumor size ranged from 7.0 to 22.5 cm （mean size was 13.5 cm） in diameter.The CT manifestations of HMH was related to the proportion and distribution of component in the masses.The masses were cystic （n =1）,cystic-solid mixed （n =6） and solid （n =3）.After contrast administration,the solid component and the septa of the mass showed enhancement while cystic component was not enhanced.Calcification was seen inside the tumor in one case.Conclusions The CT features of HMH in children are multitudinous which are related to postoperative pathological findings.With the clinical history,it is easy to distinguish HMH from the other hepatic tumors.

关 键 词：肝肿瘤 错构瘤 体层摄影术 X线计算机 病理学 

分 类 号：R735.7[医药卫生—肿瘤]