完全性Kartagener综合征合并左侧气胸、Ⅰ型呼吸衰竭1例并文献复习  

Complete Kartagener＇s syndrome with left pneumothorax and I breath prostrate：a case report and literature review

作　　者：常双喜[1] 卢春玲[1] 禹彩霞[1] 李宝珠[1] 

机构地区：[1]郑州市第一人民医院呼吸内科,450003

出　　处：《国际呼吸杂志》2014年第6期425-426,共2页International Journal of Respiration

摘　　要：目的分析Kartagener综合征的临床特点及诊治方法。方法分析1例Kartagener综合征患者的诊治过程及文献复习。结果患者，女，47岁，因反复出现呼吸道症状人院，诊断Kartagener综合征，经过对症治疗症状缓解。结论Kartagener综合征属于先天性常染色体隐性遗传性疾病，全内脏反位、支气管扩张、鼻窦炎三联征可以明确诊断，诊断主要以影像学检查为依据，无特殊治疗方法，主要为对症治疗。Objective To analyze the clinical features, diagnosis, and treatment of Kartagener＇s syndrome （KS）. Methods One case of KS was reported and the related literatures were reviewed. Results The patient with KS was a 47 years old female who had been admitted to hospital several times because of recurrent respiratory symptoms, which were relieved after symptomatic treatment. Conclusions KS is belong to congenital autosomal recessive hereditary disease. Imaging findings play important roles in the diagnosis of KS, if it has the classical triad of visceral inversion, bronchiectasis, and accessory sinusitis. Symptomatic treatment is the main methods.

关 键 词：KARTAGENER综合征 支气管扩张 内脏反位 

分 类 号：R765.4[医药卫生—耳鼻咽喉科] R56[医药卫生—临床医学]