婴儿鼻软骨间叶性错构瘤临床病理观察  

Clinicopathological observation of nasal chondromesenchymal hamartoma in infant

作　　者：夏慧[1] 王志强[2] 王宗敏[3] 

机构地区：[1]湖州市第一人民医院病理科,浙江湖州313000 [2]池州市人民医院病理科,安徽池州247000 [3]温州医科大学育英儿童医院病理科,浙江温州325000

出　　处：《实用肿瘤杂志》2014年第2期175-178,共4页Journal of Practical Oncology

摘　　要：婴儿鼻软骨间叶性错构瘤(nasal chondromesenchymal hamartoma,NCMH)1例报告及相关文献复习。新生儿表现呼吸不畅,CT扫描发现左鼻腔鼻窦囊性肿块,肿块在内镜手术切除后1年复发。病理学显示梭形间质细胞黏液背景中透明软骨岛、动脉瘤样骨囊肿区及透明变性的胶原纤维小梁。NCMH是一种罕见的破坏性的良性病变,类似恶性肿瘤。完整切除肿瘤是预防复发的关键。A case of infant nasal chondromesenchymal hamartoma （NCMH） was reported and relevant literature was reviewed. The newborn presented with shortness of breath and CT scan revealed a cystic tumor of the left nasal cavity and sinuses. The tumor was recurred 1 year after endoscopic sinus surgery. The pathology revealed that the tumor presented islands of hyaline cartilage in the mucus background of spindle cell stroma, aneurismal-like bone cyst areas and hyalinized collagenous trabeculae. NCMH is a rare destructive benign lesion, similar to malignant tumors. Complete resection of the lesion is crucial to prevent recurrence, particularly in endoscopic sinus surgery.

关 键 词：鼻肿瘤 病理学 鼻肿瘤 外科学 错构瘤 病理学 错构瘤 外科学 软骨 婴儿 

分 类 号：R739.62[医药卫生—肿瘤] R730.2[医药卫生—临床医学]